Owens Micaela, Gatson Na Tosha, Mongelluzzo Gino, Goren Oded, Newman Eric, Sandulescu Mihai Cosmin
Department of Neurology, Geisinger Medical Center, Danville, Pennsylvania, USA.
Department of Radiology, Geisinger Medical Center, Danville, Pennsylvania, USA.
Case Rep Neurol. 2021 Jul 5;13(2):434-440. doi: 10.1159/000514728. eCollection 2021 May-Aug.
Normal-pressure hydrocephalus (NPH) is a common cause of gait apraxia, cognitive impairment, and urinary incontinence in the elderly. It is usually a primary idiopathic disorder but can be secondary. We present a case of secondary NPH due to biopsy-confirmed rheumatoid meningitis initially refractory to intravenous (IV) immunotherapy. Our patient reported an excellent response right after shunting. Her gait remains normal one and a half years later. We searched PubMed for similar cases of rheumatoid meningitis with gait abnormality for additional clinicopathologic discussion. The patient's movement disorder initially improved with steroid taper. However, she developed progressive symptoms, later on, refractory to IV solumedrol and rituximab. She underwent ventriculoperitoneal shunting (VPS) and reported an outstanding outcome. This is the first reported biopsy-confirmed case of rheumatoid meningitis causing NPH to undergo shunting for immediate improvement. Previous cases of rheumatoid meningitis-associated Parkinsonism have improved with steroid induction. Although our patient's rheumatoid arthritis is now controlled, her case illustrates that NPH in autoinflammatory conditions may not recover with immune suppression alone. VPS is an option for a faster response in secondary NPH due to rheumatoid meningitis or other inflammatory disorders with progressive symptoms despite standard induction therapy.
正常压力脑积水(NPH)是老年人步态失用、认知障碍和尿失禁的常见原因。它通常是原发性特发性疾病,但也可能是继发性的。我们报告一例经活检证实为类风湿性脑膜炎导致的继发性NPH病例,该病例最初对静脉注射(IV)免疫治疗无效。我们的患者在分流术后立即报告了良好的反应。一年半后她的步态仍保持正常。我们在PubMed上搜索了类似的类风湿性脑膜炎伴步态异常的病例,以进行更多的临床病理讨论。患者的运动障碍最初随着类固醇减量而改善。然而,后来她出现了进行性症状,对静脉注射甲泼尼龙和利妥昔单抗无效。她接受了脑室腹腔分流术(VPS),并报告了出色的结果。这是首例经活检证实的类风湿性脑膜炎导致NPH并通过分流术立即改善的病例。先前报道的类风湿性脑膜炎相关帕金森综合征病例通过类固醇诱导治疗有所改善。尽管我们患者的类风湿性关节炎现已得到控制,但她的病例表明,自身炎症性疾病中的NPH可能无法仅通过免疫抑制恢复。对于因类风湿性脑膜炎或其他炎症性疾病导致的继发性NPH,尽管进行了标准的诱导治疗但仍有进行性症状,VPS是一种能更快产生反应的选择。