Alhabib Salman F
College of Medicine, King Abdullah Ear Specialist Center, King Saud University, Riyadh, SAU.
Cureus. 2021 Jul 27;13(7):e16654. doi: 10.7759/cureus.16654. eCollection 2021 Jul.
Inner ear malformation is a congenital anomaly associated with prelingual sensory neural hearing loss in the pediatric population. This is a case report of bilateral radiologically diagnosed cochlear aplasia in a child who underwent unilateral left cochlear implantation with audiological results at one-year follow-up after surgery. Sixteen months after the cochlear implantation surgery, the child could produce 200 words and say a sentence with two words. In certain cases of inner ear malformation, the subgrouping of cystic cavity can be difficult and should not delay the trial of cochlear implant provided an acceptable anatomical appearance of the inner ear with cochleovestibular nerve existence and a proper electrode used for implantation.
内耳畸形是一种与儿科人群中舌前感觉神经性听力损失相关的先天性异常。本文报告一例经放射学诊断为双侧耳蜗发育不全的儿童病例，该患儿接受了左侧单侧人工耳蜗植入手术，并在术后一年进行了听力随访。人工耳蜗植入手术后16个月，该儿童能够说出200个单词，并能说出一个由两个单词组成的句子。在某些内耳畸形病例中，对囊性腔进行亚组分类可能很困难，并且只要内耳具有可接受的解剖外观、存在耳蜗前庭神经且使用了合适的植入电极，就不应延迟人工耳蜗植入试验。
