Jeong Sung-Wook, Kim Lee-Suk
Department of Otolaryngology-Head and Neck Surgery, College of Medicine, Dong-A University, Busan, Korea.
Acta Otolaryngol. 2012 Sep;132(9):910-5. doi: 10.3109/00016489.2012.675627. Epub 2012 Jun 12.
Children with cochlear aplasia can achieve favorable speech perception abilities from cochlear implantation (CI) by inserting an electrode array into the vestibule if an audiological response is reliably demonstrated before surgery by behavioral audiometry and objective measures.
The purpose of this study was to evaluate the surgical outcome of CI in children with cochlear aplasia.
The medical records of 454 children who underwent CI at the Dong-A University Hospital between January 1994 and September 2011 were reviewed. The prevalence of cochlear aplasia and the preoperative evaluations, operative findings, and postoperative speech perception abilities of implanted children with cochlear aplasia were evaluated.
The implanted children with cochlear aplasia accounted for 2% of those with inner ear malformations and 0.4% of all pediatric cochlear implantees. They showed audiological responses in preoperative electrophysiologic tests, and the eighth nerve was present in magnetic resonance imaging. The electrode array was inserted into the vestibule through an oval window after removing the stapes or through a transmastoid labyrinthotomy site. Electrical compound action potential and electrical auditory brainstem response tests showed clear neural responses after implantation. The hearing thresholds of the implanted ear improved to 25 dB HL and the children achieved significant open set speech perception abilities.
对于耳蜗发育不全的儿童，如果在手术前通过行为测听和客观测量可靠地证明有听力学反应，那么通过将电极阵列插入前庭进行人工耳蜗植入（CI）可获得良好的言语感知能力。
本研究的目的是评估人工耳蜗植入对耳蜗发育不全儿童的手术效果。
回顾了1994年1月至2011年9月在东亚大学医院接受人工耳蜗植入的454名儿童的病历。评估了耳蜗发育不全的患病率以及植入人工耳蜗的发育不全儿童的术前评估、手术发现和术后言语感知能力。
植入人工耳蜗的耳蜗发育不全儿童占内耳畸形儿童的2%，占所有小儿人工耳蜗植入者的0.4%。他们在术前电生理测试中表现出听力学反应，并且在磁共振成像中显示有第八神经。在移除镫骨后通过卵圆窗或通过经乳突迷路切开术部位将电极阵列插入前庭。植入后电复合动作电位和电听觉脑干反应测试显示出清晰的神经反应。植入耳的听力阈值提高到25 dB HL，并且儿童获得了显著的开放集言语感知能力。
