Department of Obstetrics and Gynaecology, B. P. Koirala Institute of Health Sciences, Dharan, Nepal.
JNMA J Nepal Med Assoc. 2020 Oct 15;58(230):805-808. doi: 10.31729/jnma.5043.
Obstructed Hemivagina and Ipsilateral Renal Anomaly syndrome is a rare obstructive uterovaginal anomaly involving both mesonephric and paramesonephric ducts. It usually presents after menarche with non-specific symptoms like pelvic pain, dysmenorrhea, or paravaginal mass and examination findings of paravaginal or pelvic mass. Because of non-specific symptoms and signs, the diagnosis is usually overlooked, which leads to complications like endometriosis, tubo-ovarian abscess compromising patient’s fertility, and quality of life. Therefore, in presence of these nonspecific clinical features along with imaging findings of uterine didelphys and unilateral renal agenesis, this syndrome should be considered in the diagnosis. We present a case of a 17-year-old lady with Obstructed Hemivagina and Ipsilateral Renal Anomaly syndrome, diagnosed by finding of paravaginal mass on examination and uterine didelphys with ipsilateral renal agenesis in USG and managed successfully by resection of vaginal septum. Keywords: ipsilateral renal anomaly;paravaginal mass;uterovaginal anomaly.
单侧阴道闭锁并同侧肾发育不全综合征是一种罕见的涉及中肾管和副中肾管的阴道阻塞性畸形。它通常在初潮后出现，表现为非特异性症状，如盆腔疼痛、痛经或阴道旁肿块，以及阴道旁或盆腔肿块的检查结果。由于症状和体征不典型，诊断通常被忽视，导致子宫内膜异位症、输卵管卵巢脓肿等并发症，影响患者的生育能力和生活质量。因此，对于这些非特异性临床特征，加上影像学检查发现子宫双角和单侧肾发育不全，应考虑诊断为该综合征。我们报告了一例 17 岁女性，患有单侧阴道闭锁并同侧肾发育不全综合征，通过检查发现阴道旁肿块，超声检查发现子宫双角和同侧肾发育不全，成功通过阴道纵隔切除术进行治疗。关键词：同侧肾发育不全；阴道旁肿块；阴道-子宫畸形。
