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OHVIRA：双子宫、盲端半阴道和同侧肾缺如：MRI的优势

OHVIRA: Uterus didelphys, blind hemivagina and ipsilateral renal agenesis: Advantage MRI.

作者信息

Bajaj Sunil K, Misra Ritu, Thukral Brij B, Gupta Rohini

机构信息

Department of Radiodiagnosis, Safdarjung Hospital and VM Medical College, New Delhi, India.

出版信息

J Hum Reprod Sci. 2012 Jan;5(1):67-70. doi: 10.4103/0974-1208.97811.

DOI:10.4103/0974-1208.97811
PMID:22870020
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3409925/
Abstract

We present here a case of an uncommon complex uterine anomaly - Obstructed HemiVagina with Ipsilateral Renal Agenesis (OHVIRA), also known as Herlyn-Werner-Wunderlich syndrome in a 14-year-old girl along with sonographic (trans-abdominal and trans labial), and MRI findings. The patient underwent surgery wherein imaging findings were confirmed. An MRI has proved to be of great help in correct diagnosis avoiding surgical interventions/ laparoscopy, which were needed in past to diagnose this rare anomaly. We also discuss the development of this anomaly with the help of a relatively new theory of uro-genital development by Acien and review the literature.

摘要

我们在此呈现一例罕见的复杂子宫畸形病例——梗阻性半阴道并同侧肾缺如（OHVIRA），在一名14岁女孩中出现，同时展示了超声检查（经腹和经阴唇）及MRI检查结果。该患者接受了手术，术中证实了影像学检查结果。事实证明，MRI对准确诊断有很大帮助，避免了过去诊断这种罕见畸形所需的手术干预/腹腔镜检查。我们还借助阿西安提出的相对较新的泌尿生殖系统发育理论讨论了这种畸形的发生，并对相关文献进行了综述。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/50e234c9bd78/JHRS-5-67-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/6da40830138e/JHRS-5-67-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/b6bd745fbd88/JHRS-5-67-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/e751c4d19635/JHRS-5-67-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/319b972fe8e9/JHRS-5-67-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/15653bec9fdb/JHRS-5-67-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/433f800f1181/JHRS-5-67-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/50e234c9bd78/JHRS-5-67-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/6da40830138e/JHRS-5-67-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/b6bd745fbd88/JHRS-5-67-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/e751c4d19635/JHRS-5-67-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/319b972fe8e9/JHRS-5-67-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/15653bec9fdb/JHRS-5-67-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/433f800f1181/JHRS-5-67-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dc57/3409925/50e234c9bd78/JHRS-5-67-g007.jpg

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