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Progressive Encephalomyelitis with Rigidity and Myoclonus and Myasthenia Gravis Comorbid Status with Thymoma.

作者信息

Ogawa Takashi, Ogaki Kotaro, Daida Kensuke, Nishimaki Takayasu, Ando Maya, Kawajiri Sumihiro, Wada Ryo, Noda Kazuyuki, Hattori Nobutaka, Okuma Yasuyuki

机构信息

Department of Neurology Juntendo University Shizuoka Hospital Izunokuni Shizuoka Japan.

Department of Neurology Juntendo University School of Medicine Tokyo Japan.

出版信息

Mov Disord Clin Pract. 2021 Sep 3;8(Suppl 1):S11-S13. doi: 10.1002/mdc3.13293. eCollection 2021 Aug.

DOI:10.1002/mdc3.13293
PMID:34514036
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8414492/
Abstract
摘要

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Progressive Encephalomyelitis with Rigidity and Myoclonus and Myasthenia Gravis Comorbid Status with Thymoma.伴有强直和肌阵挛的进行性脑脊髓炎及合并胸腺瘤的重症肌无力状态
Mov Disord Clin Pract. 2021 Sep 3;8(Suppl 1):S11-S13. doi: 10.1002/mdc3.13293. eCollection 2021 Aug.
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Thymoma-associated Progressive Encephalomyelitis with Rigidity and Myoclonus (PERM) with Myasthenia Gravis.胸腺瘤相关的伴有重症肌无力的进行性脑脊髓炎伴强直和肌阵挛(PERM)
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Commentary: Progressive Encephalomyelitis with Rigidity and Myoclonus and Myasthenia Gravis Comorbid Status with Thymoma.评论:伴有僵硬和肌阵挛的进行性脑脊髓炎与胸腺瘤合并重症肌无力状态。
Mov Disord Clin Pract. 2021 Sep 3;8(Suppl 1):S14-S15. doi: 10.1002/mdc3.13303. eCollection 2021 Aug.
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Progressive Encephalomyelitis with Rigidity and Myoclonus Resolving after Thymectomy with Subsequent Anasarca: An Autopsy Case.胸腺切除术后出现全身性水肿且僵硬和肌阵挛症状缓解的进行性脑脊髓炎:一例尸检病例
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Progressive encephalomyelitis with rigidity and myoclonus: the first pediatric case with glycine receptor antibodies.进行性脑脊髓炎伴僵硬和肌阵挛:首例甘氨酸受体抗体相关儿科病例。
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Progressive Encephalomyelitis With Rigidity and Myoclonus With Thymoma: A Case Report and Literature Review.伴胸腺瘤的进行性脑脊髓炎伴强直和肌阵挛:一例报告及文献复习
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Thymoma-associated progressive encephalomyelitis with rigidity and myoclonus successfully treated with thymectomy and intravenous immunoglobulin.胸腺切除联合静脉注射免疫球蛋白成功治疗与胸腺瘤相关的进行性脑脊髓炎伴强直和肌阵挛
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Glycine receptor antibody mediated Progressive Encephalomyelitis with Rigidity and Myoclonus (PERM): a rare but treatable neurological syndrome.甘氨酸受体抗体介导的僵人综合征伴进行性脑脊髓炎(PERM):一种罕见但可治疗的神经综合征。
Pract Neurol. 2014 Apr;14(2):123-7. doi: 10.1136/practneurol-2013-000511. Epub 2013 Apr 5.

引用本文的文献

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Progressive encephalomyelitis with rigidity and myoclonus after thymectomy in a woman with myasthenia gravis.一名重症肌无力女性胸腺切除术后发生伴有强直和肌阵挛的进行性脑脊髓炎。
Front Immunol. 2025 Apr 16;16:1563700. doi: 10.3389/fimmu.2025.1563700. eCollection 2025.
2
Commentary: Progressive Encephalomyelitis with Rigidity and Myoclonus and Myasthenia Gravis Comorbid Status with Thymoma.评论:伴有僵硬和肌阵挛的进行性脑脊髓炎与胸腺瘤合并重症肌无力状态。
Mov Disord Clin Pract. 2021 Sep 3;8(Suppl 1):S14-S15. doi: 10.1002/mdc3.13303. eCollection 2021 Aug.

本文引用的文献

1
Coexistence of Autoimmune Encephalitis and Other Systemic Autoimmune Diseases.自身免疫性脑炎与其他系统性自身免疫性疾病的共存
Front Neurol. 2019 Oct 31;10:1142. doi: 10.3389/fneur.2019.01142. eCollection 2019.
2
Thymoma-associated Progressive Encephalomyelitis with Rigidity and Myoclonus (PERM) with Myasthenia Gravis.胸腺瘤相关的伴有重症肌无力的进行性脑脊髓炎伴强直和肌阵挛(PERM)
Intern Med. 2017;56(13):1733-1737. doi: 10.2169/internalmedicine.56.7979. Epub 2017 Jul 1.
3
Myasthenia Gravis.重症肌无力
N Engl J Med. 2016 Dec 29;375(26):2570-2581. doi: 10.1056/NEJMra1602678.
4
Glycine receptor antibodies in PERM and related syndromes: characteristics, clinical features and outcomes.PERM 及相关综合征中的甘氨酸受体抗体:特征、临床特征和结局。
Brain. 2014 Aug;137(Pt 8):2178-92. doi: 10.1093/brain/awu142. Epub 2014 Jun 20.
5
Autoimmune retinopathy: a review and summary.自身免疫性视网膜病变:综述与总结
Semin Immunopathol. 2008 Apr;30(2):127-34. doi: 10.1007/s00281-008-0114-7. Epub 2008 Apr 12.