Cardiovascular Surgery, Toyohashi Heart Center, Toyohashi, Japan
Cardiovascular Surgery, Toyohashi Heart Center, Toyohashi, Japan.
BMJ Case Rep. 2021 Sep 20;14(9):e245186. doi: 10.1136/bcr-2021-245186.
Total anomalous pulmonary venous connection (TAPVC) is a rare congenital cardiac anomaly. There are a few reports of untreated TAPVC diagnosed in patients older than 60 years. Herein, we report the successful surgical treatment of TAPVC in a 70-year-old woman. A 70-year-old woman with TAPVC presented with symptoms of acute heart failure. We closed an atrial septal defect and performed tricuspid annuloplasty and commissurotomy of the pulmonary valve. Postoperative CT showed no residual shunt, and the pulmonary veins drained into the left atrium. She had an uneventful postoperative course. This report describes the case of the oldest known patient who underwent surgical treatment for TAPVC. Surviving into adulthood with little or no symptoms is uncommon in patients with TAPVC, and cases of late-onset TAPVC, such as our case, are rare. Nevertheless, close vigilance is necessary to prevent misdiagnosis in patients with this clinical presentation.
完全性肺静脉异位引流(TAPVC)是一种罕见的先天性心脏畸形。有少数未经治疗的 TAPVC 在 60 岁以上患者中被诊断的报道。在此,我们报告了一例成功治疗 70 岁女性 TAPVC 的病例。一位 70 岁女性因 TAPVC 出现急性心力衰竭症状。我们闭合了房间隔缺损,并进行了三尖瓣环成形术和肺动脉瓣交界切开术。术后 CT 显示无残余分流,肺静脉流入左心房。她术后恢复顺利。本报告描述了已知接受 TAPVC 手术治疗的最年长患者的病例。在 TAPVC 患者中,很少有成年后无症状或症状轻微的情况,像我们的病例一样,迟发性 TAPVC 非常罕见。然而,对于有这种临床表现的患者,仍需要密切监测,以防误诊。