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成人 T 细胞白血病/淋巴瘤的心脏累及。

Cardiac Involvement of Adult T Cell Leukemia/Lymphoma.

机构信息

Department of Hematology and Rheumatology, Kagoshima University Hospital, Japan.

Department of Hematology, Ikeda Hospital, Japan.

出版信息

Intern Med. 2022 Apr 1;61(7):1055-1057. doi: 10.2169/internalmedicine.7925-21. Epub 2021 Sep 18.

Abstract

Adult T-cell leukemia/lymphoma (ATL) is a refractory T-cell lymphoma with variable clinical profiles, commonly exhibiting extra-nodal involvement. The myocardial involvement of ATL is often detected at an autopsy; however, the development of a symptomatic cardiac mass due to ATL is extremely rare. We herein report a 65-year-old man with ATL who developed cardiac symptoms due to a rapidly enlarging left ventricular mass soon after the initiation of systemic chemotherapy. We also summarize previously reported cases of symptomatic ATL with cardiac involvement.

摘要

成人 T 细胞白血病/淋巴瘤(ATL)是一种难治性 T 细胞淋巴瘤,具有不同的临床特征,通常表现为结外累及。ATL 的心肌累及通常在尸检时被发现;然而,由于 ATL 而导致有症状的心包肿块的发展极为罕见。在此,我们报告了一例 65 岁男性 ATL 患者,在开始全身化疗后不久,由于左心室肿块迅速增大而出现心脏症状。我们还总结了之前报道的有症状 ATL 合并心脏受累的病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e186/9038455/4ad72967dc46/1349-7235-61-1055-g001.jpg

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