Ghemigian Adina, Carsote Mara, Sandru Florica, Petca Razvan-Cosmin, Oproiu Ana-Maria, Petca Aida, Valea Ana
Department of Endocrinology, 'Carol Davila' University of Medicine and Pharmacy, 050474 Bucharest, Romania.
Department of Endocrinology, 'C. I. Parhon' National Institute of Endocrinology, 011863 Bucharest, Romania.
Exp Ther Med. 2021 Nov;22(5):1219. doi: 10.3892/etm.2021.10653. Epub 2021 Aug 26.
This is a narrative review focusing on neuroendocrine neoplasia (NEN) and bone status, in terms of metastases and osteoporosis/fractures. One fifth of NEN have skeletal dissemination, this affinity being regulated by intrinsic tumor factors such as the C-X-C chemokine receptor 4 (CXCR4). Bone colonization impairs the patient quality of life, representing a surrogate of reduced survival. Patients with NEN without bone metastases may exhibit low bone mineral density, perhaps carcinoid-related osteoporosis, yet not a standardized cause of osteoporosis. Case-finding strategies to address bone health in NEN with a good prognosis are lacking. Contributors to fractures in NEN subjects may include: menopausal status and advanced age, different drugs, induced hypogonadism, malnutrition, malabsorption (due to intestinal resection, carcinoid syndrome), hypovitaminosis D, impaired glucose profile (due to excessive hormones such as glucagon, somatostatinoma or use of somatostatin analogues), various corticoid regimes, and high risk of fall due to sarcopenia. Pheocromocytoma/paraganglioma involve bone through malignant forms (bone is an elective site) and potential secondary osteoporosis due to excessive hormonal content and increased sympathetic activity which is a key player of bone microarchitecture/quality as reflected by low Trabecular Bone Score. Glucocorticoid osteoporosis is related to NEN-associated ectopic Cushing syndrome. Currently, there are a lack of studies to emphasis that excessive gut-derivate serotonin in NENs with carcinoid syndrome is a specific activator of bone loss thus a contributor to carcinoid-related osteoporosis.
这是一篇叙述性综述,重点关注神经内分泌肿瘤(NEN)与骨骼状况,涉及转移以及骨质疏松症/骨折方面。五分之一的NEN会发生骨骼转移,这种倾向受诸如C-X-C趋化因子受体4(CXCR4)等内在肿瘤因子调控。骨转移会损害患者生活质量,是生存预后不良的一个标志。无骨转移的NEN患者可能表现出低骨密度,或许是类癌相关的骨质疏松症,但并非骨质疏松症的标准化病因。目前缺乏针对预后良好的NEN患者进行骨骼健康筛查的策略。NEN患者发生骨折的相关因素可能包括:绝经状态和高龄、不同药物、继发性性腺功能减退、营养不良、吸收不良(由于肠道切除、类癌综合征)、维生素D缺乏、血糖异常(由于胰高血糖素、生长抑素瘤等激素过多或使用生长抑素类似物)、各种皮质激素治疗方案以及肌肉减少症导致的高跌倒风险。嗜铬细胞瘤/副神经节瘤通过恶性形式累及骨骼(骨骼是一个好发部位),并且由于激素含量过高和交感神经活动增加可能导致继发性骨质疏松,而低小梁骨评分反映出交感神经活动是骨微结构/质量的关键因素。糖皮质激素性骨质疏松与NEN相关的异位库欣综合征有关。目前,缺乏研究强调类癌综合征的NEN中肠道衍生的5-羟色胺过多是骨质流失的特定激活剂,因此是类癌相关骨质疏松症的一个促成因素。