Yamada H, Masuyama Y, Maesaki S, Yasuoka A, Koga H, Kohno S, Kanda T, Hara K, Ayabe H, Tomita M
Second Department of Internal Medicine, School of Medicine, Nagasaki University.
Nihon Kyobu Shikkan Gakkai Zasshi. 1991 May;29(5):622-6.
A 45-year-old man complained of fever and bloody sputum. Chest X-ray films showed a round opacity in the left hilum. He developed massive hemoptysis (500 ml) and emergency embolization of the bronchial artery was performed. Pulmonary artery aneurysm and thrombosis were detected angiographically, and fiberoptic bronchoscopy revealed a reddish irregular eminence of the left main bronchus and lingulate++ ++ bronchus. These sites could have been the bleeding sites. Because of recurrent hemoptysis, left pneumonectomy was performed 26 days after the massive hemoptysis. Pathological findings showed panarteritis, luminal thromboembolism of the pulmonary artery and markedly dilated vessels of the bronchial wall. He developed genital ulceration after the operation and these findings suggested incomplete vasculo-Behçet's disease with rare pulmonary involvement. The disease is now well-controlled by corticosteroid therapy 27 months after the operation.
一名45岁男性主诉发热和咯血。胸部X线片显示左肺门有一圆形致密影。他出现大量咯血（500毫升），遂进行了支气管动脉紧急栓塞术。血管造影检查发现肺动脉瘤和血栓形成，纤维支气管镜检查显示左主支气管和舌叶支气管有红色不规则隆起。这些部位可能是出血部位。由于反复咯血，在大量咯血26天后进行了左肺切除术。病理检查结果显示为全动脉炎、肺动脉腔内血栓栓塞以及支气管壁血管明显扩张。术后他出现了生殖器溃疡，这些表现提示为不完全性血管性白塞病，肺部受累罕见。术后27个月，该疾病目前通过皮质类固醇治疗得到了良好控制。
