新生儿上气道梗阻的罕见病因：先天性鼻梨状孔狭窄于偏远医疗机构就诊病例
An infrequent cause of neonatal upper airway obstruction: Congenital nasal pyriform aperture stenosis presenting to a remote facility.
作者信息
Lahiff Tahne Joseph, Sotutu Viliame, Sarachandran Smrdhi, Speed Lucas, Saddi Vishal
机构信息
James Cook University School of Medicine and Dentistry Douglas QLD 4811 Australia.
North West Hospital and Health Service Paediatric Department Mount Isa QLD Australia.
出版信息
Pediatr Investig. 2021 Jun 21;5(3):244-246. doi: 10.1002/ped4.12269. eCollection 2021 Sep.
INTRODUCTION
Congenital nasal pyriform aperture stenosis (CNPAS) is a rare congenital condition of structural nasal obstruction. Respiratory distress, stertor, and poor feeding are often presenting features.
CASE PRESENTATION
We report a case of a newborn diagnosed with CNPAS at 3 weeks of life. The diagnosis was missed on a nasoendoscopy at day 3 of life but was realised following a facial CT when the infant presented with ongoing symptoms of upper airway obstruction. Nasal dilation was performed successfully.
CONCLUSION
CNPAS should be considered in any neonate with upper airway obstruction. A normal nasoendoscopy does not exclude the diagnosis.
引言
先天性鼻梨状孔狭窄（CNPAS）是一种罕见的先天性鼻腔结构阻塞疾病。呼吸窘迫、鼾症和喂养困难是其常见症状。
病例报告
我们报告一例新生儿，在出生3周时被诊断为CNPAS。出生第3天的鼻内镜检查漏诊了该疾病，但当婴儿出现持续的上呼吸道阻塞症状时，面部CT检查后确诊。成功进行了鼻腔扩张术。
结论
任何患有上呼吸道阻塞的新生儿都应考虑CNPAS。鼻内镜检查结果正常并不能排除该诊断。
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