AlWatban Zaki, Nasser Mai, Al Abdullah Amal, Shajira Eman, Al Shehabi Mohammad
Ministry of Health, Riyadh, Kingdom of Saudi Arabia.
Otorhinolaryngology, Head and Neck Surgery Department, Royal Medical Service, Manama, Bahrain.
Indian J Otolaryngol Head Neck Surg. 2025 Jan;77(1):510-520. doi: 10.1007/s12070-024-05154-0. Epub 2024 Nov 20.
Congenital nasal pyriform aperture stenosis (CNPAS) is a rare disorder that causes airway obstruction in newborns and children. Patients with CNPAS mainly present with nasal obstruction, respiratory distress, feeding difficulties, and/or failure to thrive. Here, we present the case of a 1-day old male baby born with tachypnea, nasal obstruction, and congestion. Clinical examination revealed subcostal retraction and nasal obstruction. Nasal examination revealed an inability to pass the neonatal scope bilaterally and narrowing of the nostrils. Imaging revealed an isolated narrowed pyriform aperture of 4.5 mm. The patient was treated conservatively, and he showed significant improvement.
The online version contains supplementary material available at 10.1007/s12070-024-05154-0.
先天性鼻梨状孔狭窄（CNPAS）是一种罕见疾病，可导致新生儿和儿童气道阻塞。CNPAS患者主要表现为鼻塞、呼吸窘迫、喂养困难和/或生长发育迟缓。在此，我们报告一例1日龄男婴，出生时即出现呼吸急促、鼻塞和充血。临床检查发现肋下凹陷和鼻塞。鼻腔检查显示双侧无法通过新生儿鼻内镜，鼻孔变窄。影像学检查显示梨状孔孤立性狭窄，直径为4.5毫米。该患者接受了保守治疗，并取得了显著改善。
在线版本包含可在10.1007/s12070-024-05154-0获取的补充材料。
