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糖原贮积病Ib型中单核细胞功能受损。

Impaired monocyte function in glycogen storage disease type Ib.

作者信息

Ueno N, Tomita M, Ariga T, Ohkawa M, Nagano S, Takahashi Y, Arashima S, Matsumoto S

出版信息

Eur J Pediatr. 1986 Sep;145(4):312-4. doi: 10.1007/BF00439409.

DOI:10.1007/BF00439409
PMID:3464427
Abstract

Phagocyte (neutrophil and monocyte) function was evaluated in a boy with glycogen storage disease type Ib. Neutrophils were found to be defective in motility and respiratory burst and monocytes showed a defect in respiratory burst but not in motility. These results suggested that the glucose-6-phosphate transport system plays a role in the function of neutrophils and monocytes and that these two phagocytes are different from each other in their energy metabolism for motility.

摘要

对一名患有Ⅰb型糖原贮积病的男孩的吞噬细胞(中性粒细胞和单核细胞)功能进行了评估。发现中性粒细胞在运动性和呼吸爆发方面存在缺陷,而单核细胞在呼吸爆发方面存在缺陷,但在运动性方面没有缺陷。这些结果表明,6-磷酸葡萄糖转运系统在中性粒细胞和单核细胞的功能中发挥作用,并且这两种吞噬细胞在运动的能量代谢方面彼此不同。

相似文献

1
Impaired monocyte function in glycogen storage disease type Ib.糖原贮积病Ib型中单核细胞功能受损。
Eur J Pediatr. 1986 Sep;145(4):312-4. doi: 10.1007/BF00439409.
2
Defective neutrophil and monocyte functions in glycogen storage disease type Ib: a literature review.1b型糖原贮积病中性粒细胞和单核细胞功能缺陷:文献综述
Eur J Pediatr. 1993;152 Suppl 1:S33-8. doi: 10.1007/BF02072085.
3
Inflammatory bowel disease in glycogen storage disease type Ib.糖原贮积病Ib型中的炎症性肠病
J Pediatr. 1986 Jul;109(1):55-9. doi: 10.1016/s0022-3476(86)80572-8.
4
A convenient diagnostic function test of peripheral blood neutrophils in glycogen storage disease type Ib.Ⅰb型糖原贮积病中外周血中性粒细胞的一种便捷诊断功能试验。
Pediatr Res. 1999 Jun;45(6):881-5. doi: 10.1203/00006450-199906000-00018.
5
Impairment of calcium mobilization in phagocytic cells in glycogen storage disease type 1b.1b型糖原贮积病中吞噬细胞钙动员受损。
Eur J Pediatr. 1993;152 Suppl 1:S39-43. doi: 10.1007/BF02072086.
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MR imaging of bone marrow in glycogen storage disease type IB in children and young adults.儿童及青年期ⅠB型糖原贮积病骨髓的磁共振成像
AJR Am J Roentgenol. 2001 Aug;177(2):421-5. doi: 10.2214/ajr.177.2.1770421.
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Impaired metabolic function and signaling defects in phagocytic cells in glycogen storage disease type 1b.1b型糖原贮积病中吞噬细胞的代谢功能受损和信号缺陷。
J Clin Invest. 1990 Jul;86(1):196-202. doi: 10.1172/JCI114684.
8
Interferon-gamma corrects the respiratory burst defect in vitro in monocyte-derived macrophages from glycogen storage disease type 1b patients.干扰素-γ可在体外纠正1b型糖原贮积病患者单核细胞衍生巨噬细胞中的呼吸爆发缺陷。
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Defective neutrophil chemotaxis with variant ichthyosis, hyperimmunoglobulinemia E, and recurrent infections.伴有鱼鳞病变异型、高免疫球蛋白E血症和反复感染的中性粒细胞趋化性缺陷。
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10
Partial correction of neutrophil dysfunction by oral galactose therapy in glycogen storage disease type Ib.口服半乳糖疗法对Ⅰb型糖原贮积病中性粒细胞功能障碍的部分纠正作用
Int Immunopharmacol. 2017 Mar;44:216-225. doi: 10.1016/j.intimp.2017.01.020. Epub 2017 Jan 23.

引用本文的文献

1
Glycogen storage diseases: new perspectives.糖原贮积病:新观点
World J Gastroenterol. 2007 May 14;13(18):2541-53. doi: 10.3748/wjg.v13.i18.2541.
2
Defective neutrophil and monocyte functions in glycogen storage disease type Ib: a literature review.1b型糖原贮积病中性粒细胞和单核细胞功能缺陷:文献综述
Eur J Pediatr. 1993;152 Suppl 1:S33-8. doi: 10.1007/BF02072085.
3
Impairment of calcium mobilization in phagocytic cells in glycogen storage disease type 1b.1b型糖原贮积病中吞噬细胞钙动员受损。

本文引用的文献

1
A method of studying leukocytic functions in vivo.一种在体内研究白细胞功能的方法。
Ann N Y Acad Sci. 1955 Mar 24;59(5):757-805. doi: 10.1111/j.1749-6632.1955.tb45983.x.
2
Regulation of the immune response--role of the macrophage.免疫反应的调节——巨噬细胞的作用
N Engl J Med. 1980 Nov 13;303(20):1153-6. doi: 10.1056/NEJM198011133032005.
3
Impaired metabolic function of polymorphonuclear leukocytes in glycogen storage disease Ib.糖原贮积病Ib型中多形核白细胞代谢功能受损。
Eur J Pediatr. 1993;152 Suppl 1:S39-43. doi: 10.1007/BF02072086.
4
Impaired metabolic function and signaling defects in phagocytic cells in glycogen storage disease type 1b.1b型糖原贮积病中吞噬细胞的代谢功能受损和信号缺陷。
J Clin Invest. 1990 Jul;86(1):196-202. doi: 10.1172/JCI114684.
Eur J Pediatr. 1983 Sep;140(4):329-30. doi: 10.1007/BF00442674.
4
The macrophage as an effector cell.作为效应细胞的巨噬细胞。
N Engl J Med. 1980 Sep 11;303(11):622-6. doi: 10.1056/NEJM198009113031106.
5
Short communication. Glycogenosis Ib: neutrophil microbicidal defects due to impaired hexose monophosphate shunt.简短通讯。糖原贮积病Ib型:由于磷酸己糖旁路受损导致的中性粒细胞杀菌缺陷。
Pediatr Res. 1984 Mar;18(3):297-9. doi: 10.1203/00006450-198403000-00019.
6
Glycogen storage disease type Ib.Ⅰb型糖原贮积病
Eur J Pediatr. 1983 Sep;140(4):283-8. doi: 10.1007/BF00442664.
7
Neutropenia in a patient with type IB glycogen storage disease: in vitro response to lithium chloride.1B型糖原贮积病患者的中性粒细胞减少症:对氯化锂的体外反应
J Pediatr. 1980 Dec;97(6):944-6. doi: 10.1016/s0022-3476(80)80428-8.
8
Neutropenia and impaired neutrophil migration in type IB glycogen storage disease.1型糖原贮积病中的中性粒细胞减少及中性粒细胞迁移受损
J Pediatr. 1980 Dec;97(6):906-10. doi: 10.1016/s0022-3476(80)80418-5.
9
Type Ib glycogen storage disease is caused by a defect in the glucose-6-phosphate translocase of the microsomal glucose-6-phosphatase system.I型糖原贮积病是由微粒体葡萄糖-6-磷酸酶系统的葡萄糖-6-磷酸转运酶缺陷引起的。
J Biol Chem. 1980 Sep 25;255(18):8381-4.
10
Neutropenia and impaired neutrophil function in glycogenosis type Ib.糖原贮积病Ib型中的中性粒细胞减少及中性粒细胞功能受损。
J Inherit Metab Dis. 1984;7(4):151-4. doi: 10.1007/BF01805597.