Department of Cardiology, University of Liège Hospital, GIGA Cardiovascular Sciences, Liege, Belgium.
Acta Cardiol. 2023 Jun;78(4):459-462. doi: 10.1080/00015385.2021.1991666. Epub 2021 Oct 21.
Pericardial agenesis is a rarely seen congenital defect characterised by the partial or, more rarely complete, absence of the pericardium. Most often asymptomatic, it is usually incidentally discovered following the demonstration of heart's laevorotation on imaging, in the operating room or at autopsy. In this article, we report the case of an 80-year-old patient with asymptomatic complete pericardial agenesis fortuitous discovered. Pericardial agenesis observations are extremely uncommon reported in the literature, which substantiate its original epidemiological character. In addition, this observation brings some clinical, electrical as well as iconographic elements to better understand the pathology and raises clinical suspicions. Finally, this case report confirms the exceptionally symptomatic nature of the pathology, illustrating the irrelevance of treatment or specific follow-up.
心包发育不全是一种罕见的先天性缺陷，其特征为部分或更罕见的完全缺乏心包。大多数情况下无症状，通常在影像学、手术室或尸检中发现心脏左旋时偶然发现。在本文中，我们报告了一例 80 岁无症状完全性心包发育不全患者的偶然发现。心包发育不全的观察结果在文献中极为罕见，证实了其原始的流行病学特征。此外，这一观察结果提供了一些临床、电生理和影像学方面的元素，以更好地理解病理学，并引起临床怀疑。最后，该病例报告证实了该病理学的异常症状性质，说明了治疗或特定随访的无关性。
