Adi Kuncoro, Noegroho Bambang S, Septrina Rani, Sasotya Rm Sonny, Drajat K Dikki, Saputra Daniel
Urology Department, Hasan Sadikin Academic Medical Center, Universitas Padjadjaran Bandung, Indonesia.
Plastic Surgery Department, Hasan Sadikin Academic Medical Center, Universitas Padjadjaran Bandung, Indonesia.
Urol Case Rep. 2021 Oct 25;40:101911. doi: 10.1016/j.eucr.2021.101911. eCollection 2022 Jan.
Herlyn-Werner-Wunderlich (HWW) syndrome is difficult to diagnose. We report our first experience of fistula repair in HWW syndrome in Hasan Sadikin General Hospital Indonesia. A 12 years old girl presented with urinary retention, and was consulted to urology because the urethral meatus could not be found. MRI showed two separate uteri, cervices, and vaginas. Complete separation of vagina and urethra was done. After 2 years follow up, the patient had no complaint. HWW syndrome should be suspected in cases with pelvic pain or urinary retention during menarche period among teenagers and neonatal cases with any renal malformation.
赫林-韦纳-温德利希(HWW)综合征难以诊断。我们报告了在印度尼西亚哈桑·萨迪金综合医院对HWW综合征进行瘘管修复的首例经验。一名12岁女孩出现尿潴留,因尿道口无法找到而咨询泌尿外科。磁共振成像(MRI)显示有两个独立的子宫、宫颈和阴道。完成了阴道与尿道的完全分离。经过2年随访,患者无不适主诉。对于青少年月经初潮期出现盆腔疼痛或尿潴留的病例以及任何有肾脏畸形的新生儿病例,均应怀疑HWW综合征。