Department of Dermatology, Auckland District Health Board, Auckland, New Zealand.
Department of Dermatology, Royal Victoria Infirmary, Newcastle upon Tyne, England.
Am J Dermatopathol. 2021 Dec 1;43(12):e277-e279. doi: 10.1097/DAD.0000000000002070.
We present a case of a 74-year-old man with marked photodamage who was ultimately diagnosed with telangiectasia macularis eruptiva perstans (TMEP) of the scalp. The diagnosis was made more difficult because of the clinical and histological similarity of this case with an early angiosarcoma. TMEP is a benign and indolent rare subtype of cutaneous mastocytosis presenting clinically with red-brown telangiectatic macules, usually symmetrically distributed over the trunk and extremities. Although most cases are limited to the skin, systemic involvement can occur, and this can be a potentially life-threatening disease. Although also rare, in contrast to TMEP, cutaneous angiosarcoma is a highly malignant vascular tumor with a poor prognosis. This case highlights the importance of including TMEP on the differential diagnosis where vascular lesions of the scalp are observed.
我们报告一例 74 岁男性患者，其头皮有明显的光损伤，最终被诊断为持久性毛细血管扩张性红斑疹（TMEP）。由于该病例的临床表现和组织学与早期血管肉瘤相似，因此诊断更为困难。TMEP 是一种良性且惰性的皮肤肥大细胞增多症罕见亚型，临床上表现为红色-棕色毛细血管扩张性斑疹，通常对称分布于躯干和四肢。尽管大多数病例局限于皮肤，但也可能发生全身受累，这可能是一种潜在的危及生命的疾病。虽然也罕见，但与 TMEP 相反，皮肤血管肉瘤是一种高度恶性的血管肿瘤，预后不良。本病例强调了在观察头皮血管病变时将 TMEP 纳入鉴别诊断的重要性。
