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左心室心肌致密化不全作为晕厥的罕见病因

Left Ventricular Noncompaction as a Rare Cause of Syncope.

作者信息

Ojemolon Pius E, Evbayekha Endurance O, Odion Jesse, Bello Jeremiah, Shaka Hafeez

机构信息

Internal Medicine, John H. Stroger, Jr. Hospital of Cook County, Chicago, USA.

Internal Medicine, Stella Obasanjo Isolation Centre, Benin, NGA.

出版信息

Cureus. 2021 Nov 9;13(11):e19409. doi: 10.7759/cureus.19409. eCollection 2021 Nov.

DOI:10.7759/cureus.19409
PMID:34909328
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8659991/
Abstract

Left ventricular noncompaction (LVNC) is a relatively rare myocardial disorder which is characterized by trabeculations and deep intertrabecular recesses within the left ventricle. LVNC is often asymptomatic but may present with heart failure, arrhythmias, or systemic thromboembolism. Uncommonly, patients with LVNC can present with syncope. In this article, we report one such presentation of this rare medical condition.

摘要

左心室致密化不全(LVNC)是一种相对罕见的心肌疾病,其特征是左心室内存在肌小梁和深陷的小梁间隐窝。LVNC通常无症状,但可能表现为心力衰竭、心律失常或全身性血栓栓塞。罕见的是,LVNC患者可能出现晕厥。在本文中,我们报告了这种罕见病症的一个这样的病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/1961965b44f3/cureus-0013-00000019409-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/d1d01d86c407/cureus-0013-00000019409-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/ba6f26cb3a9e/cureus-0013-00000019409-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/3bbe03a97e53/cureus-0013-00000019409-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/1961965b44f3/cureus-0013-00000019409-i04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/d1d01d86c407/cureus-0013-00000019409-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/ba6f26cb3a9e/cureus-0013-00000019409-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/3bbe03a97e53/cureus-0013-00000019409-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8e8d/8659991/1961965b44f3/cureus-0013-00000019409-i04.jpg

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本文引用的文献

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Left ventricular noncompaction-a rare cause of triad: heart failure, ventricular arrhythmias, and systemic embolic events: a case report.左心室心肌致密化不全——三联征(心力衰竭、室性心律失常和全身栓塞事件)的罕见病因:病例报告。
J Med Case Rep. 2021 Jun 8;15(1):316. doi: 10.1186/s13256-021-02862-x.
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Left ventricular noncompaction - Risk stratification and genetic consideration.左心室心肌致密化不全 - 风险分层与遗传考虑。
J Cardiol. 2020 Jan;75(1):1-9. doi: 10.1016/j.jjcc.2019.09.011. Epub 2019 Oct 17.
3
Heart Failure Secondary to Left Ventricular Non-compaction Cardiomyopathy in a 26-Year-Old Male.
一名26岁男性因左心室心肌致密化不全导致的心力衰竭
Cureus. 2018 Jul 20;10(7):e3011. doi: 10.7759/cureus.3011.
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Catastrophic stroke in a patient with left ventricular non-compaction.左心室心肌致密化不全患者发生灾难性中风。
Echo Res Pract. 2018 Sep;5(3):K59-K62. doi: 10.1530/ERP-18-0015.
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Bradycardia, Syncope, and Left Ventricular Noncompaction Cardiomyopathy.心动过缓、晕厥与左心室致密化不全心肌病
Am J Cardiol. 2017 Aug 15;120(4):716-717. doi: 10.1016/j.amjcard.2017.04.058. Epub 2017 May 30.
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Non-compaction cardiomyopathy: a genetically and clinically heterogeneous disorder.非致密化型心肌病:一种基因和临床均异质性的疾病。
Acta Cardiol. 2015 Dec;70(6):625-31. doi: 10.2143/AC.70.6.3120173.
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Left ventricular non-compaction cardiomyopathy.左心室心肌致密化不全心肌病。
Lancet. 2015 Aug 22;386(9995):813-25. doi: 10.1016/S0140-6736(14)61282-4. Epub 2015 Apr 9.
8
Isolated left ventricular non-compaction cardiomyopathy in adults.成人孤立性左心室心肌致密化不全心肌病
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9
Non-compaction cardiomyopathy: prevalence, prognosis, pathoetiology, genetics, and risk of cardioembolism.非致密化型心肌病:患病率、预后、病理病因、遗传学及心源性栓塞风险
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Defining left ventricular noncompaction using cardiac computed tomography.使用心脏计算机断层扫描定义左心室心肌致密化不全。
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