Weiss Hans-Rudolf, Lay Manuel, Best-Gittens Tamisha, Moramarco Marc, Jimeranez Mario
Schroth Best Practice Academy, Neu-Bamberg, Germany.
Koob Scolitech GmbH, Neu-Bamberg, Germany.
S Afr J Physiother. 2021 Nov 30;77(2):1588. doi: 10.4102/sajp.v77i2.1588. eCollection 2021.
This is a case report of a juvenile female patient with scoliosis following two heart surgeries for congenital heart disease (CHD).
Initially, the premenarchial female was 9 years old and had a Tanner stage 2-3 with a single thoracic curve of 65° Cobb. Because of the high risk for progression, immediate brace treatment was proposed as the father declined surgery. The patient received intensive treatment according to the Schroth Best Practice® programme and a Gensingen Brace® designed for large thoracic curves. Over the 18 months following the initial visit, she received two additional braces. As a result, the progression of the main curve was prevented. The patient continues to maintain an improved cosmetic result and is currently at a Risser 2.
Surgery performed for CHD in rare cases may lead to stiff spinal deformity as a consequence of that surgery. Progression of a severe and stiff curve was prevented during the most vulnerable phase of the pubertal growth spurt with an improved clinical result. Therefore, we assume that the patient may have a normal life in adulthood with minor restrictions only. Supported by pattern-specific high correction exercises and braces, these typical single thoracic curves can be re-compensated to a more balanced appearance, less prone to progression in adulthood.
Because of the relative high risks of spinal fusion and the long-term unknowns of such an intervention, high-impact conservative treatment should be implemented first before surgical correction is considered.
本文报告一例患有先天性心脏病(CHD)并接受了两次心脏手术的青春期女性脊柱侧弯患者。
患者表现、治疗与结果:最初,这位青春期前女性患者9岁,坦纳分期为2 - 3期,胸弯Cobb角为65°。由于进展风险高,鉴于父亲拒绝手术,建议立即进行支具治疗。患者根据施罗斯最佳实践方案以及专为大胸弯设计的根辛支具接受了强化治疗。在初诊后的18个月里,她又佩戴了两个支具。结果,主弯进展得到了预防。患者的外观持续改善,目前Risser征为2级。
因CHD进行的手术在罕见情况下可能导致脊柱僵硬畸形。在青春期生长突增最易受影响的阶段,严重僵硬的脊柱侧弯进展得到了预防,临床结果有所改善。因此,我们认为该患者成年后可能仅受到轻微限制,可过上正常生活。在特定模式的高矫正度锻炼和支具的支持下,这些典型的单胸弯可以重新调整至更平衡的外观,成年后不易进展。
鉴于脊柱融合相对较高的风险以及此类干预的长期未知因素,在考虑手术矫正之前,应首先实施高强度的保守治疗。