Lohrer R, Barran L, Kellnar S, Belohradsky B H
Monatsschr Kinderheilkd. 1986 Dec;134(12):878-80.
In an eleven year old girl Atrophodermia idiopathica et progressiva Pasini et Pierini, a rare variety of localised scleroderma developed within six months as well outlined, reddish-brown, patchy lesions without induration on her right side. The histological examination revealed perivascular inflammatory infiltrations in all corium layers, and discrete sclerosis radiating into fat tissue cells. The levels of antinuclear antibodies and C-reactive protein were both elevated. During intravenous therapy with penicillin G the skin alterations faded but did not disappear.
在一名11岁女孩身上，出现了帕西尼-皮耶里尼特发性进行性皮肤萎缩症，这是一种罕见的局限性硬皮病，在六个月内右侧出现了轮廓清晰、红棕色、斑片状且无硬结的病变。组织学检查显示所有真皮层均有血管周围炎性浸润，并有离散性硬化延伸至脂肪组织细胞。抗核抗体和C反应蛋白水平均升高。在静脉注射青霉素G治疗期间，皮肤病变消退但未消失。
