State Key Laboratory of Radiation Medicine and Protection, Cyrus Tang Medical Institute, Collaborative Innovation Center of Hematology, Soochow University, Suzhou, 215123, China.
Division of Life Sciences and Medicine, Department of Hematology, The First Affiliated Hospital of USTC, University of Science and Technology of China, Hefei, 230001, Anhui, People's Republic of China.
J Mol Histol. 2022 Apr;53(2):423-436. doi: 10.1007/s10735-021-10052-8. Epub 2021 Dec 23.
ZKSCAN3 encodes a zinc-finger transcription factor that regulates the expression of important genes and plays a significant role in tumor development, pathogenesis, and metastasis. However, its biological functions under normal physiological conditions remain largely unknown. In our previous studies, using flow cytometry, we found that the deletion of Zkscan3 may cause abnormal erythropoiesis. In this study, we found that, in a Zkscan3 knockout mice model, the number of splenic early-stage (basophilic-erythroblasts) and late-stage (chromatophilic-erythroblasts to polychromatophilic-erythroblasts through orthochromatophilic-erythroblasts) erythroblasts increased, whereas the number of late erythroblasts in the bone marrow decreased. Moreover, the phenotype was exacerbated after treating mice with phenylhydrazine (PHZ), which causes severe hemolytic anemia. In the knockout mice treated with PHZ, the percentage of reticulocyte in the peripheral blood conspicuously increased, whereas MCHC and red blood cells decreased. Then, we performed RNA-seq and quantitative-polymerase chain reaction assay and found that the expression of GATA1 and Tiam1 in erythroblasts were upregulated, whereas KLF1 was downregulated. Luciferase assays showed that Zkscan3 inhibited the transcription of GATA1 and Tiam1 and promoted the expression of KLF1. Additionally, ChIP and CO-IP results confirmed that Zkscan3 directly interacts with GATA1 and inhibits its transcriptional activity in MEL cells. Our results demonstrate, for the first time, the significant role of Zkscan3 in physiological erythropoiesis through the interaction with GATA1, both at the DNA and protein level, and with Tiam1 and KLF1 at the DNA level.
ZKSCAN3 编码一个锌指转录因子,调节重要基因的表达,在肿瘤发生、发展和转移中发挥重要作用。然而,其在正常生理条件下的生物学功能仍知之甚少。在我们之前的研究中,通过流式细胞术,我们发现 Zkscan3 的缺失可能导致红细胞生成异常。在这项研究中,我们发现 Zkscan3 敲除小鼠模型中,脾早期(嗜碱性-红细胞)和晚期(嗜硷性-红细胞至多色性-红细胞通过正硷性-红细胞)红细胞数量增加,而骨髓晚期红细胞数量减少。此外,用苯肼(PHZ)处理小鼠后,表型加重,导致严重的溶血性贫血。在 PHZ 处理的敲除小鼠中,外周血网织红细胞的百分比明显增加,而 MCHC 和红细胞减少。然后,我们进行了 RNA-seq 和定量聚合酶链反应检测,发现红细胞中 GATA1 和 Tiam1 的表达上调,而 KLF1 的表达下调。荧光素酶检测表明,Zkscan3 抑制 GATA1 和 Tiam1 的转录,并促进 KLF1 的表达。此外,ChIP 和 CO-IP 结果证实 Zkscan3 直接与 GATA1 相互作用,抑制其在 MEL 细胞中的转录活性。我们的研究结果首次证明,Zkscan3 通过与 GATA1 的相互作用,在 DNA 和蛋白质水平上以及在 DNA 水平上与 Tiam1 和 KLF1 相互作用,在生理红细胞生成中发挥重要作用。