Nagao N, Shomura I, Sawada Y
Biochem Med Metab Biol. 1987 Jun;37(3):385-8. doi: 10.1016/0885-4505(87)90052-1.
We previously found that the level of the immunoreactive activity of C1 inactivator in the plasma Duchenne-type patients with progressive muscular dystrophy was lower than that in normal boys. Therefore, we investigated the level of the C1 inactivator inhibiting activity against C1 esterase in the serum from PMD patients. The mean level of anti-esterase activity of C1 inactivator against C1 esterase in the serum from PMD was 50% lower than that of the control group (P less than 0.05).
我们之前发现，进行性肌营养不良的杜兴氏型患者血浆中C1灭活剂的免疫反应活性水平低于正常男孩。因此，我们研究了进行性肌营养不良患者血清中C1灭活剂对C1酯酶的抑制活性水平。进行性肌营养不良患者血清中C1灭活剂对C1酯酶的抗酯酶活性平均水平比对照组低50%（P小于0.05）。
