Department of Nephrology, Japanese Red Cross Ishinomaki Hospital, Ishinomaki, Japan.
Division of Nephrology, Endocrinology and Vascular Medicine, Tohoku University Graduate School of Medicine, Sendai, Japan.
CEN Case Rep. 2022 Aug;11(3):371-375. doi: 10.1007/s13730-021-00678-8. Epub 2022 Feb 2.
Granulomatosis with polyangiitis is an anti-neutrophil cytoplasmic antibody-associated vasculitis that manifests in various ways by affecting the small-sized vessels in multiple organs. Acute pleuritis and pericarditis are both rare among the different manifestations of granulomatosis with polyangiitis. The symptoms in each of the organs are often apparent at the time of diagnosis and tend to diminish with treatment. Organ damage and progression of the disease during treatment are uncommon. We encountered a patient with granulomatosis with polyangiitis who, after starting intravenous methylprednisolone pulse therapy, concurrently developed acute pleuritis and pericarditis. The patient was a 47-year-old Japanese man with myalgia in whom kidney dysfunction, proteinase 3-anti-neutrophil cytoplasmic antibody positivity, and a lung mass were detected. Granulomatosis with polyangiitis was diagnosed pathologically from a lung and a kidney biopsy. Acute pleuritis and pericarditis, which developed after the first course of intravenous methylprednisolone pulse therapy, both resolved following the second course. The present report indicates that secondary serositis such as pleuritis and pericarditis can develop in patients with granulomatosis with polyangiitis even during glucocorticoid therapy.
肉芽肿性多血管炎是一种抗中性粒细胞胞质抗体相关性血管炎,可通过影响多个器官的小血管而以多种方式表现出来。急性胸膜炎和心包炎在肉芽肿性多血管炎的不同表现中都较为罕见。在诊断时,各器官的症状通常较为明显,且往往随着治疗而减轻。在治疗过程中,器官损伤和疾病进展并不常见。我们遇到了一位患有肉芽肿性多血管炎的患者,他在开始静脉注射甲基泼尼松龙脉冲治疗后,同时并发了急性胸膜炎和心包炎。该患者为一名 47 岁的日本男性,出现了肌肉疼痛,同时检测到肾功能障碍、蛋白酶 3-抗中性粒细胞胞质抗体阳性和肺部肿块。通过对肺部和肾脏活检进行病理诊断,确诊为肉芽肿性多血管炎。在第一疗程静脉注射甲基泼尼松龙脉冲治疗后出现的急性胸膜炎和心包炎,在第二疗程后均得到缓解。本报告表明,即使在糖皮质激素治疗期间,肉芽肿性多血管炎患者也可能发生继发性浆膜炎,如胸膜炎和心包炎。