Azapagasi Ebru, Uysal Yazici Mutlu, Ari Mehmet Emre, Karakaya Rabia Sedef, Cınar Hasibe Gökçe, Tasar Mehmet, Gucer Safak
Division of Pediatric Intensive Care Unit, Dr. Sami Ulus Maternity and Children's Training and Research Hospital, Ankara, Turkey.
Division of Pediatric Cardiology, Dr. Sami Ulus Maternity and Children's Training and Research Hospital, Ankara, Turkey.
J Pediatr Intensive Care. 2020 Aug 31;11(1):77-82. doi: 10.1055/s-0040-1715849. eCollection 2022 Mar.
Cardiac myxoma is rare in children. Myxomas are exceedingly rare in infancy. Right atrial myxomas were recorded in a small number of case reports involving infants worldwide. We report the case of a 2-month-old infant with giant right atrial myxoma. The case presented to our hospital with respiratory distress, and had pericardial and pleural effusion. Diagnosis of cardiac tumor was made with the aid of computerized tomography scan and echocardiogram. The tumor size was 3.1 × 3.4 × 3.9 cm. The patient worsened rapidly and had sudden cardiac arrest which did not respond to interventions. Postmortem cardiac autopsy confirmed the diagnosis of myxoma on gross examination and histology. This article aims to focus attention to the atypical size and location of this atrial myxoma, causing diagnostic difficulty in this infant.
心脏黏液瘤在儿童中较为罕见。黏液瘤在婴儿期极为罕见。全球范围内仅有少数涉及婴儿的病例报告记录了右心房黏液瘤。我们报告一例2个月大患有巨大右心房黏液瘤的婴儿病例。该病例因呼吸窘迫就诊于我院，伴有心包和胸腔积液。借助计算机断层扫描和超声心动图诊断为心脏肿瘤。肿瘤大小为3.1×3.4×3.9厘米。患者病情迅速恶化，出现心脏骤停，对干预措施无反应。尸检心脏大体检查和组织学检查确诊为黏液瘤。本文旨在关注该心房黏液瘤非典型的大小和位置，这给该婴儿的诊断带来了困难。
