缩窄性心包炎揭示罕见的 ALH 淀粉样变性病例，其基础疾病为淋巴浆细胞淋巴瘤（华氏巨球蛋白血症）。

Constrictive Pericarditis Revealing Rare Case of ALH Amyloidosis With Underlying Lymphoplasmacytic Lymphoma (Waldenstrom Macroglobulinemia).

作者信息

Ho Vivian V, O'Sullivan Jack W, Collins William J, Ozdalga Errol, Bell Caitlin F, Shah Neil D, Krishnam Mayil S, Ozawa Michael G, Witteles Ronald M

机构信息

Stanford University School of Medicine, Stanford, California, USA.

Division of Cardiovascular Medicine, Department of Medicine, Stanford University, Stanford, California, USA.

出版信息

JACC Case Rep. 2022 Mar 2;4(5):271-275. doi: 10.1016/j.jaccas.2022.01.007.

DOI:10.1016/j.jaccas.2022.01.007

PMID:35257101

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8897150/

Abstract

We present a case of pericardial amyloidosis with associated lymphoplasmacytic lymphoma in a patient with chronic worsening shortness of breath and cough. This case highlights the wide variation in the presentation of cardiac amyloidosis, and the rare occurrence of clinically significant light-chain and heavy-chain amyloidosis in the pericardium. ().

摘要

我们报告一例心包淀粉样变性合并淋巴浆细胞淋巴瘤的病例，患者有慢性进行性加重的气短和咳嗽症状。该病例突出了心脏淀粉样变性临床表现的广泛差异，以及心包中具有临床意义的轻链和重链淀粉样变性的罕见发生情况。（）