Numan F, Cokyüksel O, Camuşcu S, Demir K, Düren M
Rontgenblatter. 1986 Jul;39(7):191-2.
In 1958 Caroli described the syndrome of congenital, either segmental or involving the entire bile duct system, saccular extensions of the intrahepatic bile ducts. He differentiated between two types of this disease pattern. The first form concerns pure cystic dilatations of the intrahepatic bile ducts, whereas the second one is combined with hepatic fibrosis and portal hypertension. Both types are characterised by cystic dilatations in the kidneys and in the extrahepatic bile ducts, pancreas and spleen.
1958年，卡罗利描述了先天性综合征，该综合征可为节段性，也可累及整个胆管系统，表现为肝内胆管的囊状扩张。他区分了这种疾病模式的两种类型。第一种类型是单纯的肝内胆管囊性扩张，而第二种类型则伴有肝纤维化和门静脉高压。两种类型的特征均为肾脏、肝外胆管、胰腺和脾脏出现囊性扩张。
