Department of Clinical Neurophysiology, Institute of Psychiatry and Neurology, Sobieskiego 9, 02-957, Warsaw, Poland.
Second Department of Neurology, Institute of Psychiatry and Neurology, Warsaw, Poland.
Acta Neurol Belg. 2022 Jun;122(3):745-751. doi: 10.1007/s13760-022-01915-2. Epub 2022 Mar 23.
Most neurodegenerative and chronic liver disorders are associated with sleep disturbances (SD). SD may be expected to occur in patients with Wilson's disease (WD), an inherited disorder of copper metabolism that mostly affects the liver and brain; however, there is a lack of observations, particularly in treatment-naïve WD patients.
We evaluated SD in 19 newly diagnosed treatment-naïve WD patients. All patients completed the Beck Depression Inventory (BDI), the Athens Insomnia Scale (AIS) and the Epworth Sleepiness Scale (ESS), and underwent nightlong video polysomnography (vPSG). Results of vPSG in WD patients were compared with results from 19 sex- and age-matched healthy controls.
Depressive symptoms were not reported by patients on routine examination although three patients were diagnosed with mild depression. No patients reported SD during routine examination; three patients had insomnia according to the AIS and all patients scored 0 on the ESS. Despite the lack of reporting of SD by patients, significant differences were observed between WD patients and controls following vPSG analysis: WD patients had shorter mean total sleeping time (366.2 vs. 451.7 min), a lower percentage of rapid-eye movement (15.4 vs. 20.6%), longer sleep latency (36.7 vs. 10.4 min) and lower sleep efficiency (76.2 vs. 93.8%) (all P ≤ 0.01). SD tended to be worse in patients with neurological WD compared with hepatic WD.
As SD may precede depression and severely affect quality of life, our findings suggest that patients with WD should be screened for SD with suitable methods.
大多数神经退行性疾病和慢性肝脏疾病都与睡眠障碍(SD)有关。SD 可能发生在威尔逊病(WD)患者中,这是一种铜代谢遗传疾病,主要影响肝脏和大脑;然而,目前观察到的病例较少,尤其是在未经治疗的 WD 患者中。
我们评估了 19 例新诊断的未经治疗的 WD 患者的 SD。所有患者均完成贝克抑郁量表(BDI)、雅典失眠量表(AIS)和 Epworth 嗜睡量表(ESS),并进行了整夜视频多导睡眠图(vPSG)检查。将 WD 患者的 vPSG 结果与 19 名性别和年龄匹配的健康对照者的结果进行比较。
尽管有 3 名患者被诊断为轻度抑郁,但患者在常规检查中并未报告抑郁症状。在常规检查中,没有患者报告 SD;根据 AIS,有 3 名患者患有失眠,所有患者 ESS 得分为 0。尽管患者未报告 SD,但 vPSG 分析后观察到 WD 患者与对照组之间存在显著差异:WD 患者的平均总睡眠时间更短(366.2 分钟 vs. 451.7 分钟),快速眼动(REM)百分比更低(15.4% vs. 20.6%),睡眠潜伏期更长(36.7 分钟 vs. 10.4 分钟),睡眠效率更低(76.2% vs. 93.8%)(均 P≤0.01)。与肝性 WD 相比,神经 WD 患者的 SD 倾向于更差。
由于 SD 可能先于抑郁发生,并严重影响生活质量,因此我们的研究结果表明,WD 患者应使用合适的方法筛查 SD。