Kuo Yi-Wen, Lin Jung-Chia, Tsai Wei-Hsuan
Department of Dermatology, E-Da Cancer Hospital, Kaohsiung, Taiwan.
School of Medicine, I-Shou University, Kaohsiung, Taiwan.
Arch Craniofac Surg. 2022 Apr;23(2):83-88. doi: 10.7181/acfs.2022.00101. Epub 2022 Mar 30.
Nevus sebaceous of Jadassohn is a congenital cutaneous hamartoma with epidermal, sebaceous, follicular, and apocrine structures that usually appears at birth or in early childhood. It has the potential to generate a variety of secondary neoplasms of different lineages, and the risk increases with patient age. Although multiple neoplasms may occasionally arise within the same lesion, the coexistence of more than five secondary tumors is extremely rare. Here we report a case of seven secondary tumors including syringocystadenoma papilliferum, desmoplastic trichilemmoma, sebaceoma, trichoblastoma, pigmented trichoblastoma, sebaceous adenoma, and tumor of follicular infundibulum arising within a nevus sebaceous. The complete diagnosis relies on the histopathological analysis of multipoint biopsies and delicate pathological sections.
Jadassohn皮脂腺痣是一种先天性皮肤错构瘤,具有表皮、皮脂腺、毛囊和顶泌汗腺结构,通常在出生时或幼儿期出现。它有可能产生各种不同谱系的继发性肿瘤,且风险随患者年龄增加而升高。虽然同一病变内偶尔可能出现多个肿瘤,但同时存在五个以上继发性肿瘤极为罕见。在此,我们报告一例发生在皮脂腺痣内的七个继发性肿瘤病例,包括乳头状汗管囊腺瘤、促结缔组织增生性外毛根鞘瘤、皮脂腺瘤、毛母细胞瘤、色素性毛母细胞瘤、皮脂腺腺瘤和毛囊漏斗部肿瘤。完整的诊断依赖于多点活检和精细病理切片的组织病理学分析。