Belabbes Fatima Zahra, Benfaida Amine, Nawal Bouknani, El Idrissi Lamghari Abdennaceur, Rouibaa Fedoua
Gastroenterology and Proctology, Faculty of Medicine, Mohammed VI University of Health Sciences (UM6SS) Cheikh Khalifa International University Hospital, Casablanca, MAR.
Radiology, Faculty of Medicine, Mohammed VI University of Health Sciences (UM6SS) Cheikh Khalifa International University Hospital, Casablanca, MAR.
Cureus. 2022 Feb 19;14(2):e22383. doi: 10.7759/cureus.22383. eCollection 2022 Feb.
Low phospholipid-associated cholelithiasis (LPAC) is a genetic disease responsible for the development of intrahepatic lithiasis. It is retained in the presence of two of the following three criteria: age of onset of biliary symptoms less than 40 years; echogenic intrahepatic images or microlithiasis; and the recurrence of biliary clinical signs after cholecystectomy. The majority of clinical situations are simple and not serious, but some complicated forms may require more invasive endoscopic or surgical treatments. By presenting two case studies, we illustrated and summarized the different aspects of this entity.
低磷脂相关胆石症(LPAC)是一种导致肝内结石形成的遗传性疾病。当符合以下三项标准中的两项时即可诊断:胆汁症状发作年龄小于40岁;肝内回声图像或微结石;胆囊切除术后胆汁临床体征复发。大多数临床情况较为简单且不严重,但一些复杂形式可能需要更具侵入性的内镜或手术治疗。通过两个病例研究,我们阐述并总结了该疾病的不同方面。