Bandres Dervis, Prada Carlos, Soto José, Dávila Marielvis, Bandres Maria, García Victoria
Division of Gastroenterology and Hepatology, Department of Medicine, Centro Medico Docente La Trinidad, Caracas, Venezuela.
Division of Pediatric Surgery, Department of Surgery, Centro Medico Docente La Trinidad, Caracas, Venezuela.
ACG Case Rep J. 2022 Apr 7;9(4):e00755. doi: 10.14309/crj.0000000000000755. eCollection 2022 Apr.
Hirschsprung disease (HD) may affect short, ultrashort, or long segments of the rectum. Invasive endoscopy has gained popularity in its treatment. We report a case of a 9-year-old girl diagnosed with HD at 4-year-old, at which time she underwent a myectomy. Nonetheless, because of the persistence of clinical symptoms such as bowel movements every 5-7 days and abdominal distension, per-anal endoscopic myotomy was recommended. An anterograde myotomy in the posterior wall was performed to the circular layer of the muscularis propria. At the 3-year follow-up, she has continued daily bowel movements without laxatives.
先天性巨结肠(HD)可累及直肠的短段、超短段或长段。侵入性内镜检查在其治疗中越来越受欢迎。我们报告一例9岁女孩,4岁时被诊断为HD,当时她接受了肌切除术。尽管如此,由于仍存在临床症状,如每5-7天排便一次和腹胀,建议进行经肛门内镜肌切开术。在固有肌层的环形层进行后壁顺行肌切开术。在3年的随访中,她无需使用泻药即可每日排便。