Center for Psychiatric Genetics, NorthShore University HealthSystem, Evanston, IL 60201, United States of America; Department of Human Genetics, The University of Chicago, Chicago, IL 60637, United States of America.
Center for Psychiatric Genetics, NorthShore University HealthSystem, Evanston, IL 60201, United States of America; Department of Psychiatry and Behavioral Neuroscience, The University of Chicago, Chicago, IL 60637, United States of America.
Schizophr Res. 2024 Nov;273:39-61. doi: 10.1016/j.schres.2022.04.003. Epub 2022 Apr 20.
Recent genome-wide association studies (GWAS) and whole-exome sequencing of neuropsychiatric disorders, especially schizophrenia, have identified a plethora of common and rare disease risk variants/genes. Translating the mounting human genetic discoveries into novel disease biology and more tailored clinical treatments is tied to our ability to causally connect genetic risk variants to molecular and cellular phenotypes. When combined with the Clustered Regularly Interspaced Short Palindromic Repeats (CRISPR)/CRISPR-associated (Cas) nuclease-mediated genome editing system, human induced pluripotent stem cell (hiPSC)-derived neural cultures (both 2D and 3D organoids) provide a promising tractable cellular model for bridging the gap between genetic findings and disease biology. In this review, we first conceptualize the advances in understanding the disease polygenicity and convergence from the past decade of iPSC modeling of different types of genetic risk factors of neuropsychiatric disorders. We then discuss the major cell types and cellular phenotypes that are most relevant to neuropsychiatric disorders in iPSC modeling. Finally, we critically review the limitations of iPSC modeling of neuropsychiatric disorders and outline the need for implementing and developing novel methods to scale up the number of iPSC lines and disease risk variants in a systematic manner. Sufficiently scaled-up iPSC modeling and a better functional interpretation of genetic risk variants, in combination with cutting-edge CRISPR/Cas9 gene editing and single-cell multi-omics methods, will enable the field to identify the specific and convergent molecular and cellular phenotypes in precision for neuropsychiatric disorders.
最近的全基因组关联研究(GWAS)和神经精神疾病(尤其是精神分裂症)的全外显子组测序已经确定了大量常见和罕见的疾病风险变异体/基因。将不断增加的人类遗传发现转化为新的疾病生物学和更具针对性的临床治疗方法,取决于我们将遗传风险变异体与分子和细胞表型因果联系起来的能力。当与簇状规律间隔短回文重复序列(CRISPR)/CRISPR 相关(Cas)核酸酶介导的基因组编辑系统结合使用时,人类诱导多能干细胞(hiPSC)衍生的神经培养物(二维和三维类器官)为弥合遗传发现与疾病生物学之间的差距提供了一个有前途的可行细胞模型。在这篇综述中,我们首先从过去十年使用 iPSC 对不同类型的神经精神疾病遗传风险因素进行建模的角度,概念化理解疾病多基因性和汇聚的进展。然后,我们讨论了在 iPSC 建模中与神经精神疾病最相关的主要细胞类型和细胞表型。最后,我们批判性地审查了 iPSC 神经精神疾病建模的局限性,并概述了需要实施和开发新方法来系统地增加 iPSC 系和疾病风险变异体的数量。充分扩大规模的 iPSC 建模以及对遗传风险变异体的更好功能解释,结合最先进的 CRISPR/Cas9 基因编辑和单细胞多组学方法,将使该领域能够为神经精神疾病确定精确的特定和汇聚的分子和细胞表型。