Pandya Radhika H, Barad Hardev V, Raghunandan G C, Trivedi Bhadra Y
Department of Radiodiagnosis, Shree Krishna Hospital and Pramukhswami Medical College, Karamsad, Gujarat, India.
Department of Surgery, Shree Krishna Hospital and Pramukhswami Medical College, Karamsad, Gujarat, India.
J Family Med Prim Care. 2022 Apr;11(4):1528-1531. doi: 10.4103/jfmpc.jfmpc_1251_21. Epub 2022 Mar 18.
Pheochromocytomas are rare chromaffin cell tumors of adrenal medulla (90%) that secrete catecholamines. Among children, the average age of presentation is 11-13 years, with a male preponderance of 2:1. Symptoms may be caused by catecholamine overproduction, local pressure, or metastasis. Sustained hypertension is the most common symptom. Elevated circulating catecholamines can cause cardiovascular alterations such as coronary vasospasm, ventricular and supraventricular arrhythmias, and dilated cardiomyopathy, precipitating in cardiogenic shock. We present a rare case of cardiogenic shock as the initial presentation of a bilateral pheochromocytoma in a child.
嗜铬细胞瘤是肾上腺髓质（90%）罕见的嗜铬细胞瘤，可分泌儿茶酚胺。在儿童中，发病的平均年龄为11 - 13岁，男性与女性的比例为2:1。症状可能由儿茶酚胺分泌过多、局部压迫或转移引起。持续性高血压是最常见的症状。循环儿茶酚胺水平升高可导致心血管改变，如冠状动脉痉挛、室性和室上性心律失常以及扩张型心肌病，进而引发心源性休克。我们报告一例罕见病例，一名儿童双侧嗜铬细胞瘤最初表现为心源性休克。
