处理失代偿性艾森曼格综合征危重症患者的挑战。
Challenges in managing a critically ill patient with decompensated Eisenmenger syndrome.
机构信息
Anaesthesia and Intensive Care Unit, Hospital Queen Elizabeth, Kota Kinabalu, Malaysia.
Anaesthesiology and Intensive Care Department, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Kota Kinabalu, Sabah, Malaysia.
出版信息
BMJ Case Rep. 2022 May 17;15(5):e245549. doi: 10.1136/bcr-2021-245549.
Abstract
Eisenmenger syndrome (ES) is the most severe form of pulmonary arterial hypertension and is associated with congenital heart disease. ES itself is a challenging condition to manage, further compounded if the patient is critically ill and acutely decompensated. We share our experience of managing a critically ill adult patient with ES who presented with acute decompensation due to sepsis.
摘要
艾森曼格综合征（Eisenmenger syndrome，ES）是肺动脉高压最严重的形式，与先天性心脏病相关。ES 本身的管理极具挑战性，如果患者病情危重且急性失代偿，情况将更为复杂。我们分享了一例因脓毒症导致急性失代偿的危重 ES 成年患者的管理经验。
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