Pournazari Mehran, Assar Shirin, Mohamadzadeh Dena, Mahdian Maryam, Soltani Setareh
Rheumatology Department, Clinical Research Development Center, Imam Reza Hospital, Kermanshah University of Medical Sciences, Kermanshah, Iran.
Student Research Committee, Kermanshah University of Medical Sciences, Kermanshah, Iran.
Egypt Heart J. 2022 May 21;74(1):40. doi: 10.1186/s43044-022-00277-7.
Angiosarcoma is a malignant rare tumor that originates from vascular endothelial cells that cover lymphatic or blood vessels. Cardiac angiosarcoma is the most prevalent sarcoma entail the heart. It has low incidence rate and poor prognosis. Our effort through this report was raising awareness of uncommon manifestations of this disease and showing the importance of appropriate diagnosis and treatment.
We present a case of cardiac angiosarcoma in a young female whose symptoms included dyspnea and hemoptysis with a history of pericardial effusion and a past history of cardiac surgery for suspected atrial Myxoma. She had history of several hospitalizations and relapse of symptoms a few months after each hospital discharge.
The unspecific symptoms of cardiac angiosarcoma made it difficult to make in time diagnose and appropriate treatment. Awareness of unspecific presentations of cardiac angiosarcoma is necessary for proper diagnosis and treatment while delayed diagnosis may worsen the prognosis and even lead to death.
血管肉瘤是一种罕见的恶性肿瘤，起源于覆盖淋巴管或血管的血管内皮细胞。心脏血管肉瘤是累及心脏的最常见肉瘤。其发病率低，预后差。我们通过本报告旨在提高对该疾病罕见表现的认识，并展示正确诊断和治疗的重要性。
我们报告一例年轻女性心脏血管肉瘤病例，其症状包括呼吸困难和咯血，有心包积液病史，既往因疑似心房黏液瘤接受过心脏手术。她有多次住院史，每次出院后几个月症状复发。
心脏血管肉瘤的非特异性症状使其难以及时诊断和进行适当治疗。认识心脏血管肉瘤的非特异性表现对于正确诊断和治疗很有必要，而延迟诊断可能会使预后恶化，甚至导致死亡。
