Masroor Taleaa, Chappell Ava Ganson, Shahzad Farooq
Aga Khan University, Karachi, Pakistan.
Lurie Children's Hospital, Northwestern University Feinberg School of Medicine, Chicago, IL.
Eplasty. 2022 May 5;22:e12. eCollection 2022.
Osteogenesis imperfecta (OI) is a rare metabolic bone disorder in which collagen production is impaired. Patients have brittle bones that are prone to fracture with minor trauma. Whereas most of the fractures occur in the spine and extremities, fractures of the craniofacial bones are less common.
This report describes the management of a 14-year-old boy with OI type 1 who sustained mandible fractures from an assault. Management consisted of open reduction and internal fixation of the parasymphyseal and angle fractures and closed reduction and mandibulomaxillary fixation of the subcondylar fracture.
Surgery resulted in return of premorbid occlusion and good jaw function. Removal of plates and screws was performed 10 months later without incident.
This case report discusses the unique anesthetic, surgical, and postoperative considerations for managing mandible fractures in patients with OI.
成骨不全症(OI)是一种罕见的代谢性骨病,其中胶原蛋白生成受损。患者骨骼脆弱,轻微创伤即可导致骨折。虽然大多数骨折发生在脊柱和四肢,但颅面骨骨折较少见。
本报告描述了一名14岁1型成骨不全症男孩因袭击导致下颌骨骨折的治疗情况。治疗包括对髁突间骨折进行切开复位内固定以及对髁突下骨折进行闭合复位和颌间固定。
手术使患者恢复了病前的咬合关系,颌功能良好。10个月后顺利取出钢板和螺钉。
本病例报告讨论了成骨不全症患者下颌骨骨折治疗中独特的麻醉、手术及术后注意事项。