Department of Radiology and Imaging, Indira Gandhi Memorial Hospital, Male, Republic of Maldives.
Department of Emergency Medicine, Indira Gandhi Memorial Hospital, Male, Republic of Maldives.
JNMA J Nepal Med Assoc. 2022 Mar 11;60(247):303-305. doi: 10.31729/jnma.6266.
Primitive neuroectodermal tumour is a poorly differentiated small round cell neoplasm that primarily affects children and is very rarely seen in adults. Peripheral primitive neuroectodermal tumours are rare compared to the central type and resemble soft tissue sarcoma. Primitive neuroectodermal tumours involving the subcutaneous tissue are rare and only a few cases involving the subcutaneous tissue of the anterior abdominal wall have been reported. However, no cases involving the subcutaneous tissue of the shoulder region have been reported. We report the case of a peripheral primitive neuroectodermal tumour arising from subcutaneous tissue of the right shoulder in a young adult.
case report; magnetic resonance imaging; neuroectodermal tumour; neuron-specific enolase; subcutaneous tissue.
原始神经外胚层肿瘤是一种分化不良的小圆细胞肿瘤,主要影响儿童,在成人中极为罕见。与中枢型相比,外周原始神经外胚层肿瘤较为罕见,类似于软组织肉瘤。累及皮下组织的原始神经外胚层肿瘤罕见,仅报道了少数几例累及前腹壁皮下组织的病例。然而,尚未有报道涉及肩部的皮下组织。我们报告了一例青年成人右肩部皮下组织起源的外周原始神经外胚层肿瘤。
病例报告;磁共振成像;神经外胚层肿瘤;神经元特异性烯醇化酶;皮下组织。