Al-Khreisat Mutaz Jamal, Hussain Faezahtul Arbaeyah, Abdelfattah Ali Mahmoud, Almotiri Alhomidi, Al-Sanabra Ola Mohammed, Johan Muhammad Farid
Department of Haematology, School of Medical Sciences, Universiti Sains Malaysia, Kubang Kerian 16150, Kelantan, Malaysia.
Department of Pathology, School of Medical Sciences, Universiti Sains Malaysia, Kubang Kerian 16150, Kelantan, Malaysia.
Cancers (Basel). 2022 Jun 4;14(11):2799. doi: 10.3390/cancers14112799.
Lymphomas are heterogeneous malignant tumours of white blood cells characterised by the aberrant proliferation of mature lymphoid cells or their precursors. Lymphomas are classified into main types depending on the histopathologic evidence of biopsy taken from an enlarged lymph node, progress stages, treatment strategies, and outcomes: Hodgkin and non-Hodgkin lymphoma (NHL). Moreover, lymphomas can be further divided into subtypes depending on the cell origin, and immunophenotypic and genetic aberrations. Many factors play vital roles in the progression, pathogenicity, incidence, and mortality rate of lymphomas. Among NHLs, peripheral T cell lymphomas (PTCLs) are rare lymphoid malignancies, that have various cellular morphology and genetic mutations. The clinical presentations are usually observed at the advanced stage of the disease. Many recent studies have reported that the expressions of NOTCH1, GATA3, and c-MYC are associated with poorer prognosis in PTCL and are involved in downstream activities. However, questions have been raised about the pathological relationship between these factors in PTCLs. Therefore, in this review, we investigate the role and relationship of the NOTCH1 pathway, transcriptional factor GATA3 and proto-oncogene c-MYC in normal T cell development and malignant PTCL subtypes.
淋巴瘤是白细胞的异质性恶性肿瘤,其特征为成熟淋巴细胞或其前体细胞的异常增殖。根据取自肿大淋巴结的活检组织病理学证据、进展阶段、治疗策略及预后,淋巴瘤主要分为霍奇金淋巴瘤和非霍奇金淋巴瘤(NHL)。此外,淋巴瘤还可根据细胞起源、免疫表型及基因异常进一步分为不同亚型。许多因素在淋巴瘤的进展、致病性、发病率及死亡率中起着至关重要的作用。在非霍奇金淋巴瘤中,外周T细胞淋巴瘤(PTCL)是罕见的淋巴系统恶性肿瘤,具有多种细胞形态和基因突变。临床表现通常出现在疾病晚期。最近许多研究报道,NOTCH1、GATA3和c-MYC的表达与外周T细胞淋巴瘤预后较差相关,并参与下游活动。然而,关于这些因素在外周T细胞淋巴瘤中的病理关系仍存在疑问。因此,在本综述中,我们研究了NOTCH1信号通路、转录因子GATA3和原癌基因c-MYC在正常T细胞发育及恶性外周T细胞淋巴瘤亚型中的作用及关系。