Guadalupi Pamela, Gessi Marco, Massimi Luca, Caldarelli Massimo, Gaudino Simona
UOC Radiodiagnostica e Neuroradiologia, Dipartimento di Diagnostica per Immagini, Radioterapia, Oncologia ed Ematologia, Fondazione Policlinico Universitario A. Gemelli IRCCS, Rome, Italy.
UOC Radiodiagnostica e Neuroradiologia, Dipartimento di Diagnostica per Immagini, Radioterapia, Oncologia ed Ematologia, Istituto di Radiologia, Università Cattolica del Sacro Cuore, Rome, Italy.
Indian J Radiol Imaging. 2022 Feb 28;32(1):127-131. doi: 10.1055/s-0041-1741044. eCollection 2022 Mar.
We present the first case of clival cystic chordoma with extradural location, transdural transgression, and moderate bone involvement in a 10-year-old girl. Chordoma showed unconventional appearances on computed tomography (CT) and magnetic resonance imaging (MRI), due to cystic components, extradural space location with extensive intradural extension, moderate superficial bone involvement. Surgery confirmed the extradural location and histopathological examination revealed cystic chordoma. MRI and CT findings were not characteristic for a single lesion; differential diagnoses included cystic lesions such as epidermoid and dermoid cyst, ecchordosis physaliphora, and benign notochordal cell tumors.
我们报告了首例发生于一名10岁女孩的斜坡囊性脊索瘤，该肿瘤位于硬膜外，经硬膜侵犯，伴有中度骨质受累。由于存在囊性成分、位于硬膜外间隙并伴有广泛的硬膜内延伸以及中度浅表骨质受累，脊索瘤在计算机断层扫描（CT）和磁共振成像（MRI）上表现出非典型外观。手术证实了肿瘤位于硬膜外，组织病理学检查显示为囊性脊索瘤。MRI和CT表现对于单一病变不具有特征性；鉴别诊断包括表皮样囊肿和皮样囊肿、脊索样囊肿、良性脊索细胞瘤等囊性病变。
