Charan Bheru Dan, Agarwal Sushant, Singh Ekamjot, Jain Savyasachi, Das Sumanta, Garg Ajay, Sebastian Leve Joseph Devarajan, Singh Manmohan
Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India.
Department of Diagnostic and Interventional Radiology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
Asian J Neurosurg. 2024 Oct 10;20(1):138-142. doi: 10.1055/s-0044-1791581. eCollection 2025 Mar.
Intradural prepontine chordoma is an extremely rare entity and depicts benign features with no recurrence and has a good prognosis as compared with bone endogenous chordoma. Radiologically, it may mimic an epidermoid cyst and present an imaging challenge. Here we present a case of a middle adolescent girl who presented with headache along with limb and facial weakness. A nonenhancing, diffusion-restricting, predominantly intradural cystic-appearing mass lesion was seen in the prepontine cistern. Initially, an epidermoid cyst was suspected, but histopathology revealed it to be a chordoma. Destruction of the clivus is important and chordoma should be included in differential diagnosis.
桥前池硬膜内脊索瘤是一种极其罕见的疾病，表现为良性特征，无复发，与骨内生性脊索瘤相比预后良好。在放射学上，它可能类似表皮样囊肿，带来影像学诊断挑战。在此，我们报告一例青春期中期女孩，她因头痛伴肢体和面部无力就诊。在桥前池可见一个无强化、弥散受限、主要呈硬膜内囊肿样的肿块病变。最初怀疑为表皮样囊肿，但组织病理学显示为脊索瘤。斜坡破坏很重要，脊索瘤应列入鉴别诊断范围。
