Dulam Vipin, Keshavamurthy Suresh, Kumaran Maruti, Hota Partha, Gutierrez Carlos, Kashem Mohammed Abul, Toyoda Yoshiya
Temple University Hospital 3401 N Broad St Philadelphia, Philadelphia, PA 19140 USA.
Temple University Lewis Katz School of Medicine, 3500 N Broad St, Philadelphia, PA 19140 USA.
Indian J Thorac Cardiovasc Surg. 2022 Jul;38(4):438-441. doi: 10.1007/s12055-022-01348-9. Epub 2022 Apr 7.
Esophageal dysmotility and dysphagia are well known in patients with scleroderma. Interstitial lung disease (ILD) in these patients is an indication for lung transplantation but is considered high risk in many centers. This report is an attempt to highlight how anatomical causes can contribute to dysphagia in such patients and complicate the post-operative course after lung transplantation. Such a finding is uncommon in this subset of patients and use of suitable imaging can help in arriving at the diagnosis. We present a patient following lung transplantation for scleroderma related ILD with an aberrant right subclavian artery compressing the esophagus in a vice like grip. Imaging is the key to prompt diagnosis and management.
食管动力障碍和吞咽困难在硬皮病患者中很常见。这些患者的间质性肺疾病（ILD）是肺移植的指征，但在许多中心被认为是高风险的。本报告旨在强调解剖学原因如何导致此类患者出现吞咽困难，并使肺移植后的术后病程复杂化。这一发现在此类患者亚组中并不常见，使用合适的影像学检查有助于做出诊断。我们报告一例因硬皮病相关ILD接受肺移植的患者，其右锁骨下动脉异常，像老虎钳一样压迫食管。影像学检查是快速诊断和管理的关键。
