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Continuous Hepatogonodal and Splenogonogal Fusion: A Rare Cause of Bilateral Intra-Abdominal Testis in an 18-Month-Old Boy.

作者信息

Durmuş Gül, Boybeyi-Turer Ozlem, Özcan Hatice Nursun, Gözmen Onur, Demirbilek Hüseyin, Soyer Tutku

机构信息

Department of Pediatric Surgery, Hacettepe Universitesi Tip Fakultesi, Ankara, Turkey.

Department of Pediatric Radiology, Hacettepe Universitesi Tip Fakultesi, Ankara, Turkey.

出版信息

European J Pediatr Surg Rep. 2022 Jun 25;10(1):e80-e83. doi: 10.1055/s-0042-1747671. eCollection 2022 Jan.

DOI:10.1055/s-0042-1747671
PMID:35761905
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9233567/
Abstract

The fusion of gonadal structures with internal organs is very rare. The close proximity between the left gonad and spleen during embryogenesis may result in splenogonadal fusion (SGF). Moreover, the trapping of hepatocyte-destined mesenchyme cells in gonads is defined as hepatogonadal fusion (HGF). The fusion of gonads with intra-abdominal organs may be continuous and may impair testicular descent during the prenatal period. We herein report an 18-month-old boy presented with bilateral nonpalpable testis due to concomitant continuous HGF and SGF. To our knowledge, this is the first case of concomitant HGF and SGF in a boy with bilateral intra-abdominal testis. Laparoscopic excision of fibrous cords and orchidopexy can be achieved despite continuous fusions.

摘要

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引用本文的文献

1
The continuous type of splenogonadal fusion: A rare case report and literature review.连续性脾性腺融合:一例罕见病例报告及文献复习
Int J Surg Case Rep. 2023 Nov;112:109006. doi: 10.1016/j.ijscr.2023.109006. Epub 2023 Nov 4.

本文引用的文献

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Hepatogonadal fusion.
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