Steinmetz A P, Rappaport A, Nikolov G, Priel I E, Chamovitz D L, Dolev E
Department of Nuclear Medicine, Edith Wolfson Medical Center, Holon, Israel.
J Nucl Med. 1997 Jul;38(7):1153-5.
Splenogonadal fusion (SGF) is a rare congenital malformation characterized by fusion of the spleen and a gonad (almost always the left one) frequently associated with orofacial and/or limb developmental abnormalities. Only 125 cases were reported between 1883 and 1994. This report concerns a case of SGF in a 20-yr-old woman with an accidental finding of a splenic space-occupying lesion protruding into the lower abdomen in ultrasound and CT. Radiocolloid spleen scintigraphy and SPECT proved to be the best procedure to establish the correct diagnosis of SGF. As SGF is often asymptomatic, more liberal use of splenic scintigraphy is suggested in patients with congenital limb and/or orofacial anomalies. SGF should be included among the differential diagnoses of left abdominal, pelvic or scrotal masses.
脾性腺融合（SGF）是一种罕见的先天性畸形，其特征是脾脏与性腺（几乎总是左侧性腺）融合，常伴有口面部和/或肢体发育异常。1883年至1994年间仅报告了125例。本报告涉及一名20岁女性的SGF病例，该患者在超声和CT检查中意外发现脾脏占位性病变突入下腹部。放射性胶体脾闪烁显像和单光子发射计算机断层扫描（SPECT）被证明是建立SGF正确诊断的最佳方法。由于SGF通常无症状，建议对先天性肢体和/或口面部异常患者更广泛地使用脾闪烁显像。SGF应列入左腹部、盆腔或阴囊肿块的鉴别诊断之中。
