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单纯疱疹病毒性脑炎的罕见并发症:完全性克莱-伯二氏综合征。

Unusual complication of Herpes simplex encephalitis: complete Klüver-Bucy syndrome.

机构信息

Neurology Service, Internal Medicine Department, Hospital Central Dr Ignacio Morones Prieto, San Luis Potosi, Mexico.

Neurology Service, Internal Medicine Department, Hospital Central Dr Ignacio Morones Prieto, San Luis Potosi, Mexico

出版信息

BMJ Case Rep. 2022 Jul 11;15(7):e250745. doi: 10.1136/bcr-2022-250745.

Abstract

Klüver-Bucy syndrome is a rare neurobehavioral disorder caused by a bilateral temporal lobe lesion affecting the hippocampus and amygdala; clinically characterised by hyperorality, hypermetamorphosis, placidity, altered sexual behaviour, eating, disorders and visual impairment, agnosia and amnesia. However, the complete syndrome is rarely seen, and diagnosis does not require all the symptoms to be manifested simultaneously.We describe a patient who developed a complete Klüver-Bucy syndrome secondary to bilateral temporal involvement due to herpetic encephalitis.

摘要

克莱-伯尔-布西综合征是一种罕见的神经行为障碍,由双侧颞叶损伤引起,影响海马体和杏仁核;临床上表现为过度摄食、过度变形、温顺、性行为改变、进食障碍、视力障碍、认知障碍和遗忘症。然而,完整的综合征很少见,诊断并不需要所有症状同时表现出来。我们描述了一位患者,由于疱疹性脑炎导致双侧颞叶受累,继发出现完全克莱-伯尔-布西综合征。

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