Zupan Matej, Lavrič Alenka, Pižem Jože, Andrejčič Katrina Novak
Eye Hospital, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Institute of Pathology, Medical Faculty University of Ljubljana, Ljubljana, Slovenia.
Case Rep Ophthalmol Med. 2022 Jul 4;2022:4840380. doi: 10.1155/2022/4840380. eCollection 2022.
To report a patient with a very rare variant of iris melanoma that grows in the shape of a ring (ring melanoma). A 65-year-old patient was examined because of a pigmented lesion on the sclera. After a complete ophthalmic and ultrasound examination, a ring melanoma was diagnosed. Enucleation of the affected eye was performed, and histology report confirmed iris ring melanoma. This type of malignancy represents an exceedingly rare variant of uveal melanoma, and because of atypical clinical picture, it can be easily overlooked or misdiagnosed, which often delays adequate treatment. Gonioscopy, transillumination, and ultrasound help us to recognize and diagnose ring melanoma. Suspicion should be raised with a clinical picture that shows unilateral pigmentary glaucoma. The objective of this presentation is to describe and outline the challenging diagnosis and management of this rare disease entity.
报告一例患有非常罕见的呈环状生长的虹膜黑色素瘤（环状黑色素瘤）患者。一名65岁患者因巩膜色素沉着病变接受检查。经过全面的眼科和超声检查后，诊断为环状黑色素瘤。对患眼进行了眼球摘除术，组织学报告证实为虹膜环状黑色素瘤。这种恶性肿瘤是葡萄膜黑色素瘤极其罕见的一种变体，由于临床表现不典型，很容易被忽视或误诊，这常常会延误适当的治疗。前房角镜检查、透照法和超声有助于我们识别和诊断环状黑色素瘤。对于表现为单侧色素性青光眼的临床症状应提高警惕。本报告的目的是描述和概述这种罕见疾病实体具有挑战性的诊断和管理。
