Igala Marielle, Helley Ondo Graziella Dolorès, Lentombo Léonie Esther Ledaga, Rerambiah Léonard Kouegnigan, Lacombe Stéphane Diop, Ba Josaphat Iba, Boguikouma Jean Bruno
Service de Médecine Interne, Centre Hospitalier Universitaire de Libreville, Libreville, Gabon.
Département de Médecine Interne et Spécialités Médicales, Université des Sciences de la Santé, Libreville, Gabon.
Pan Afr Med J. 2022 Apr 12;41:294. doi: 10.11604/pamj.2022.41.294.28686. eCollection 2022.
Sickle cell disease is a genetic disease transmitted as an autosomal recessive trait. Since September 2016, at the University Hospital Center of Libreville (UHCL) hematology consultation dedicated to adult patients with sickle cell disease was offered. This was the occasion to conduct this study, the purpose of which was to describe the socio-demographic and economic profile of patients followed up on a regular basis. We conducted a retrospective, descriptive and non-comparative study in the Department of Internal Medicine at the UHCL, from September 2016 to June 2019. Patients aged 18 years and older with homozygous sickle cell disease who had been followed up during the study period, were able to answer questions and had undergone at least three haematology consultations were included in the study. A total of 88 patients out of 233 met the inclusion criteria during the study period; women predominated. The sex ratio was 0.5 and the average age of patients was 30.4 ± 7.8 years, 42% had a higher education level, 88.6% had health insurance that allowed 31.8% of them to take care of themselves, in addition to their monthly income. Sickle cell disease was an obstacle in patients daily and professional lives but they got support from family and friends. This study shows that patients with sickle cell disease who attend follow-up visits are integrated into society. Most of them have an education level that allow them to understand their illness and a health insurance which can help them manage their illness.
镰状细胞病是一种作为常染色体隐性性状遗传的疾病。自2016年9月起，利伯维尔大学医院中心（UHCL）开设了专门针对成年镰状细胞病患者的血液学咨询门诊。借此机会开展了本研究，其目的是描述定期接受随访的患者的社会人口统计学和经济状况。我们于2016年9月至2019年6月在UHCL内科进行了一项回顾性、描述性且非对比性的研究。纳入研究的对象为年龄在18岁及以上、患有纯合子镰状细胞病、在研究期间接受过随访、能够回答问题且至少接受过三次血液学咨询的患者。在研究期间，233名患者中有88名符合纳入标准；女性占多数。性别比为0.5，患者的平均年龄为30.4±7.8岁，42%的患者具有高等教育水平，88.6%的患者拥有医疗保险，这使得其中31.8%的患者除了月收入外还能自行负担医疗费用。镰状细胞病对患者的日常生活和职业生活构成了障碍，但他们得到了家人和朋友的支持。这项研究表明，接受随访的镰状细胞病患者融入了社会。他们中的大多数人具有能够让他们了解自身疾病的教育水平，并且拥有有助于他们管理疾病的医疗保险。
