Department of Orthopedics, Hind Institute of Medical Sciences, Lucknow, India.
Department of Spine Surgery, Max Superspeciality Hospital, Ghaziabad, India.
Spinal Cord Ser Cases. 2022 Jul 21;8(1):68. doi: 10.1038/s41394-022-00534-6.
Ewing's sarcoma is a Primary Neuroectodermal Tumour (PNET) commonly affecting appendicular skeleton. The involvement of axial skeleton is very rare and that too of cervical spine is rarest. We present a case of Ewing's sarcoma involving cervical spine managed surgically, and its outcome.
A 26-year-old male presented with 3-month history of neck pain and progressive motor weakness for 1 week. After clinical evaluation of sign and symptoms, MRI of cervical spine revealed a posterior neck mass over C2, C3 and C4. Because of mass effect and spinal cord compression, early surgical intervention was deemed necessary to stop progression of neurological deficit and make tissue diagnosis of lesion. On histopathological examination diagnosis of Ewing sarcoma was made. PET-CT showed C2 and C3 as primary site of involvement with no other site of involvement.
The Ewing's Sarcoma of the cervical spine is a rare occurrence and usually present in late and advanced stage. High index of suspicion should be present to make early diagnosis and prevent complications.
尤文肉瘤是一种常见于四肢骨骼的原发性神经外胚层肿瘤(PNET)。发生于中轴骨骼的情况非常罕见,而发生于颈椎的情况则最为罕见。我们报告了一例累及颈椎的尤文肉瘤,该患者接受了手术治疗,并对其结果进行了分析。
一名 26 岁男性,因颈部疼痛 3 个月,且 1 周来逐渐出现运动无力而就诊。经过对症状和体征的临床评估,颈椎 MRI 显示 C2、C3 和 C4 水平有颈部后区肿块。由于肿块效应和脊髓压迫,为了阻止神经功能缺损的进展并对病变进行组织学诊断,早期手术干预被认为是必要的。组织病理学检查诊断为尤文肉瘤。PET-CT 显示 C2 和 C3 为受累的原发性部位,无其他部位受累。
颈椎尤文肉瘤是一种罕见的疾病,通常在晚期和进展期出现。为了尽早诊断和预防并发症,应该提高对此病的警惕性。