Janowiak Piotr, Szymanowska-Narloch Amelia, Siemińska Alicja
Department of Pulmonology, Medical University of Gdańsk, Gdańsk, Poland.
Front Med (Lausanne). 2022 Jul 28;9:917973. doi: 10.3389/fmed.2022.917973. eCollection 2022.
Idiopathic pulmonary fibrosis (IPF) is a progressive, chronic disease of the lungs which is characterized by heavy symptom burden, especially in the last year of life. Despite recently established anti-fibrotic treatment IPF prognosis is one of the worst among interstitial lung diseases. In this review available evidence regarding pharmacological and non-pharmacological management of the main IPF symptoms, dyspnea and cough, is presented.
特发性肺纤维化(IPF)是一种进行性的慢性肺部疾病,其特征是症状负担沉重,尤其是在生命的最后一年。尽管最近确立了抗纤维化治疗方法,但IPF的预后在间质性肺病中是最差的之一。在这篇综述中,我们介绍了有关IPF主要症状(呼吸困难和咳嗽)的药物和非药物管理的现有证据。