Markowitz R I, Frederick W, Rosenfield N S, Seashore J H, Duray P H
Pediatr Radiol. 1987;17(4):269-72. doi: 10.1007/BF02388236.
We describe a case of a full-term infant with severe respiratory failure and pulmonary insufficiency caused by an anomaly consisting of a single, unilobar lung arising from the trachea and situated in the middle mediastinum. Plain film, echocardiogram, and surgical aspects will be described and correlated with the post mortem findings and embryologic considerations. We were unable to find a similar case reported in the literature and conclude that this rare lesion represent an intermediate form between total and unilateral pulmonary agenesis.
我们描述了一例足月婴儿，其患有严重呼吸衰竭和肺功能不全，病因是一种异常情况，即由气管发出的单个肺叶形成的单叶肺位于中纵隔。将描述X线平片、超声心动图及手术情况，并与尸检结果和胚胎学因素进行关联。我们在文献中未能找到类似病例报道，并得出结论，这种罕见病变代表了完全性肺不发育和单侧肺不发育之间的一种中间形式。
