Kakiuchi Toshihiko, Baba Yuta, Minematsu Nobuya, Doi Hirohito, Kumamoto Takashi
Department of Pediatrics, Faculty of Medicine Saga University Saga Japan.
Clin Case Rep. 2022 Sep 12;10(9):e6318. doi: 10.1002/ccr3.6318. eCollection 2022 Sep.
A 6-year-old girl with congenital portosystemic shunt presented with abnormal manganese levels and improving pulmonary hypertension even 1 year after shunt vascular ligation. As the progress after portal vein blood flow recovery varies among individuals, long-term follow-up of patients with congenital portosystemic shunt is needed.
一名患有先天性门体分流的6岁女孩,在分流血管结扎术后1年出现锰水平异常且肺动脉高压有所改善。由于门静脉血流恢复后的进展因人而异,因此需要对先天性门体分流患者进行长期随访。