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成人网膜肺泡横纹肌肉瘤:一个不寻常的部位。病例报告及文献综述。

Adult omental alveolar rhabdomyosarcoma: An unusual site. A case report and literature review.

作者信息

Chammout Anwar, Alshutaihi Mohamad Sami, Kelarji Ahmad Beshr, Naser Mouiad, Mouselli Asaad, Alyousfi Rama

机构信息

Department of Oncology, University of Aleppo, Faculty of Medicine, Aleppo, Syria.

Division of Neurology, Department of Internal Medicine, Aleppo University Hospital, Sami Alkayali Street, Almouhafaza, Aleppo, Syria.

出版信息

Ann Med Surg (Lond). 2022 Aug 18;81:104464. doi: 10.1016/j.amsu.2022.104464. eCollection 2022 Sep.

DOI:10.1016/j.amsu.2022.104464
PMID:36147128
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9486736/
Abstract

INTRODUCTION AND IMPORTANCE

Omental alveolar rhabdomyosarcoma (ARMS) in adults is a rare tumor and is not a common presentation of abdominal pain. We aim to report the eighth case of omental ARMS and perform a review of all publications that pertains to this topic.

CASE PRESENTATION

we show a case of a Mediterranean 52 year old smoker male, complaining of unbearable dull pain in the right iliac fossa. He had no relevant medical history other than general abdominal pain in the past several months.

CLINICAL DISCUSSION

the chief complaint was abdominal pain mimicking appendicitis. Physical examination showed a palpable mass in that region. Ultrasound and CT scan revealed a mass arising from the omentum. At this point we excluded the diagnosis of appendicitis and a laparotomy with biopsies sampling had been performed. The microscopical examination led to the diagnosis of alveolar rhabdomyosarcoma (ARMS). Treatment involved multidisciplinary care but the patient died during chemotherapy.

CONCLUSION

Adult rhabdomyosarcomas (RMS) are rare tumors that can arise from any soft tissue including omentum and should be taken into consideration when dealing with primary tumors that originate from the omental area. The studies and our understanding for this neoplasm are still very limited and should be expanded widely.

摘要

引言与重要性

成人网膜肺泡状横纹肌肉瘤(ARMS)是一种罕见肿瘤,并非腹痛的常见表现形式。我们旨在报告第8例网膜ARMS病例,并对所有与此主题相关的出版物进行综述。

病例介绍

我们展示了一例52岁的地中海地区吸烟男性病例,他主诉右下腹有难以忍受的钝痛。除了过去几个月的一般性腹痛外,他没有其他相关病史。

临床讨论

主要症状是类似阑尾炎的腹痛。体格检查显示该区域可触及肿块。超声和CT扫描显示肿块起源于网膜。此时我们排除了阑尾炎的诊断,并进行了剖腹活检取样。显微镜检查确诊为肺泡状横纹肌肉瘤(ARMS)。治疗采用多学科护理,但患者在化疗期间死亡。

结论

成人横纹肌肉瘤(RMS)是罕见肿瘤,可起源于包括网膜在内的任何软组织,在处理起源于网膜区域的原发性肿瘤时应予以考虑。对这种肿瘤的研究和我们的了解仍然非常有限,应广泛扩展。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/bacd8a10875d/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/ba2ec023fc14/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/9018fa5d26a4/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/bacd8a10875d/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/ba2ec023fc14/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/9018fa5d26a4/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c438/9486736/bacd8a10875d/gr3.jpg

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