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大网膜横纹肌肉瘤(大网膜原发性横纹肌样肿瘤):一例罕见病例报告

Omental rhabdomyosarcoma (primary rhabdoid tumor of greater omentum): a rare case report.

作者信息

Pathak Priyank, Nautiyal Mayank, Sachan P K, Shirazi Nadia

机构信息

Department of General Surgery, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University (SRHU), Jollygrant, Doiwala, Dehradun 248140 India.

出版信息

Surg Case Rep. 2015;1(1):73. doi: 10.1186/s40792-015-0077-6. Epub 2015 Sep 2.

DOI:10.1186/s40792-015-0077-6
PMID:26366369
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4560155/
Abstract

The greater omentum is an uncommon location for primary tumors. Metastatic tumors of the omentum are common. In contrast, primary tumors of the omentum are very rare. Sporadic cases of primary rhabdomyosarcoma (RMS) arising in the abdomen have been reported, but these cases are limited almost exclusively to the pediatric population. We report a well-documented case of primary intra-abdominal RMS in a 21-year-old man who presented with complaints of abdominal pain and lump in left hypochondrium region. Imaging revealed it to be a large mass in the left hypochondrium region displacing the bowel loops. Further investigations revealed omental RMS. The mass had originated from the greater omentum and was excised. Our case is doing well and is presently receiving chemotherapy.

摘要

大网膜是原发性肿瘤的罕见部位。网膜转移性肿瘤很常见。相比之下,原发性网膜肿瘤非常罕见。已有腹部散发性原发性横纹肌肉瘤(RMS)病例的报道,但这些病例几乎仅限于儿科人群。我们报告一例有充分记录的21岁男性原发性腹腔内RMS病例,该患者主诉左季肋区腹痛和肿块。影像学检查显示左季肋区有一巨大肿块,推移肠袢。进一步检查发现为网膜RMS。肿块起源于大网膜并已切除。我们的病例情况良好,目前正在接受化疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/01025725f3a8/40792_2015_77_Fig5_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/56e77eadad5b/40792_2015_77_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/2f7b0a5f6101/40792_2015_77_Fig2_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/759f5d8967d3/40792_2015_77_Fig3_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/7c906d05dbae/40792_2015_77_Fig4_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/01025725f3a8/40792_2015_77_Fig5_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/56e77eadad5b/40792_2015_77_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/2f7b0a5f6101/40792_2015_77_Fig2_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/759f5d8967d3/40792_2015_77_Fig3_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/7c906d05dbae/40792_2015_77_Fig4_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7e3c/4883121/01025725f3a8/40792_2015_77_Fig5_HTML.jpg

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本文引用的文献

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